A rachnoid cysts are fluid-filled suprasellar arachnoid cyst (SACs) surrounded by a transparent arachnoid membrane. Prevalence in children is estimated at 1 to 3%. 1 Most arachnoid cysts are asymptomatic and do not need specific treatment. SACs represent 1 to 20% of all arachnoid cysts. Our case is classified as an SAC-1 subtype 2 (43% of all SACs). It is originated from an expansion of the diencephalic leaf of the Liliequist membrane, explaining its upward growth until the appearance of obstructive hydrocephalus. Minimally invasive treatment of arachnoid cysts by surgical endoscopic fenestrations took over invasive craniotomies, especially when hydrocephalus is associated, as it provides natural fluid spaces to navigate deep into the brain, allowing to restore cerebrospinal fluid (CSF) dynamics between all compartments. Early recognition of developmental delays and cognitive impairment is of paramount importance in pediatric neurology as many causes can be amenable to treatment with reversible neurological deficits. Our case illustrates an uncommon symptomatic presentation of a benign entity (Fig). The positive outcome is related to the recognition of the clinical decline and the successful restoration of CSF dynamics.