Endoscopic, Single-Catheter Treatment of Dandy-Walker Syndrome Hydrocephalus: Technical Case Report and Review of Treatment Options

Abstract

Optimal treatment for hydrocephalus related to Dandy-Walker syndrome (DWS) remains elusive. Patients with DWS-related hydrocephalus often require combinations of shunting systems to effectively drain both the supratentorial ventricles and posterior fossa cyst. We describe an endoscopic technique, whereby a frontally placed, single-catheter shunting system effectively drained the supratentorial and infratentorial compartments. This reduces the complexity and potential risk associated with the combined shunting systems required by so many with DWS-related hydrocephalus.

Dandy-Walker Syndrome; Clinical Analysis and Surgical Outcome

“…10 A singlecatheter shunting system efficiently drained the supratentorial and infratentorial sections has been found to be linked with abridged difficulty and possible risk allied with the shared shunting systems necessary by so many with DWM related hydrocephalus. 17 The current results harmonized with other studies in a way that shunt failure being the main problems in these patients with dual shunt with y-connector heading to a single channel for drainage.…”

Surgical Treatment of 13 Pediatric Patients with Dandy-Walker Syndrome

“…However, Asai et al [15] reported that C-P shunt plus V-P shunt surgery may lead to secondary aquaductus cerebri stenosis. On the other hand, endoscopic surgery is also used in treatment of patients with D-WS [22,28,29,30]. Weinzierl et al [30] reported that cystoventriculoperitoneal shunt placement after transtentorial endoscopic ventriculostomy was a surgical alternative in a neonate with D-WS associated aqueductal obstruction.…”

“…Weinzierl et al [30] reported that cystoventriculoperitoneal shunt placement after transtentorial endoscopic ventriculostomy was a surgical alternative in a neonate with D-WS associated aqueductal obstruction. Sikorski and Curry [29] described an endoscopic technique for hydrocephalus related to D-WS. According to the technique, a frontally placed, single-catheter shunting system effectively drained the supratentorial and infratentorial compartments.…”

Endoscopic Transaqueductal Placement of a Single-Catheter Cyst-Ventriculoperitoneal Shunt in a Neonate With Dandy-Walker Malformation-Associated Hydrocephalus -Case Report-

“…19,22) This maneuver minimizes the complexity associated with the placement of combined VP and CP shunts, avoids CP shunt-associated complications, and facilitates transtentorial ventricular pressure equalization. However, sophisticated instrumentation and relatively complicated maneuvers are required.…”