Endolymphatic sac tumour (ELST). of a rare tumour of the temporal bone, presenting as a mass in a cerebello-pontine angle

Czopek, Jacek; Waśko, Marcin; Adamek, Dariusz

doi:10.5114/fn.2013.35960

Cited by 5 publications

(3 citation statements)

References 30 publications

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“…The ELST arises in the endolymphatic sac or ducts and is considered a tumor of the temporal bone [10]. It is slow growing, locally aggressive in nature and results in the destruction of bony structures and can extend through the CP angle to the base of the skull.…”

Section: Discussionmentioning

confidence: 99%

Endolymphatic sac tumor at the cerebellopontine angle: A case report and review of literature

Alkhotani

Butt

Khalid

et al. 2019

International Journal of Surgery Case Reports

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Highlights Endolymphatic Sac tumors are very rare type of tumor reported in practice of Neurosurgery or ENT. This tumor may present in sporadic fashion or as a part of Von Hippel Lindau disease. In this case report Endolymphatic Sac Tumor of sporadic type is presented at the cerebellopontine angle in the posterior fossa of the skull. It was managed in our facility with multidisciplinary approach. The clinical presentation, investigations and management of the patient are discussed in details and a brief review of the literature has been performed.

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Section: Discussionmentioning

confidence: 99%

Endolymphatic sac tumor at the cerebellopontine angle: A case report and review of literature

Alkhotani

Butt

Khalid

et al. 2019

International Journal of Surgery Case Reports

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“…MB have to be considered in the differential diagnosis of CPA tumors. However, there are no radiographic features to differentiate MBs from other tumors in the CPA [ 30 – 32 ]. The differential diagnosis of CPA MB may be a challenge, and is based on the clinical, radiological and histopathological examination.…”

Section: Discussionmentioning

confidence: 99%

Atypical bilateral cerebellopontine angle medulloblastoma: differential diagnosis, immunohistochemical features and radiological presentation

Batista

Eulate-Beramendi

Rico

et al. 2017

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Medulloblastoma (MB) is a highly aggressive soft tissue neoplasm, classified as a primitive neuroectodermal tumor. It is the most common posterior fossa tumor in children, but occurs rarely in adults. MB accounts for approximately 20% of all primary central nervous system (CNS) tumors of childhood, while its incidence is around 1% of adult brain tumors. Most often it occurs in the cerebellum. We report a case of multicentric MB involving the bilateral cerebellopontine angle (CPA) and right cerebellar hemisphere. The tumor showed isointensity on T1/T2-weighted images, and slight hyperintensity on T2-weighted fluid-attenuated inversion-recovery (FLAIR) images. The MB had restricted diffusion on diffusion-weighted images (DWI). It was not easy to make an accurate diagnosis before biopsy. The lesion in our patient presented with atypical MR image features of medulloblastoma. To our knowledge, this is the first case of bilateral CPA MB.

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“…Диагноз основывается на клинической, рентгенологической и патологической корреляции [3]. ОЭМ возникает первоначально из эпителия ЭМ или эндолимфатических протоков и считается опухолью височной кости [4,5].…”

Section: Introductionunclassified

Endolymphatic sac tumor: rewiev of literature

et al. 2022

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Endolymphatic sac tumors are rare neoplasms of the temporal bone, histologically benign, but clinically behaves as malignant tumors causing destruction of surrounding tissues. The tumor originates from the posterior surface of petrous part of temporal bone, where endolymphatic sac is situated anatomically. The tumor causes destruction of the posterior surface of the petrous part of the temporal bone, inner ear, mastoid process, etc. Endolymphatic sac tumor can be both sporadically and in patients with von Hippel – Lindau disease. Due to the rarity of this tumor, it is easy to confuse it with other tumors, such as paraganglioma, middle ear adenoma, adenocarcinoma, papillary thyroid carcinoma or papilloma of the vascular plexus. Computed tomography (CT) and magnetic resonance imaging (MRI) are of great diagnostic importance and play an important role in planning treatment tactics. The optimal method of treatment is resection of pathologically altered tissues. In some cases (incomplete resection of tumor, the patients with concomitant diseases or inoperable cases) receive courses of X-ray or radiosurgery. If a tumor is detected in the early stages, the volume of resection can be minimized while preserving hearing and vestibular function of the inner ear. Recurrence usually happens due to difficulty to identify the extension of the tumor. Diagnosis and correct preoperative planning, with embolization if it possible, will facilitate surgery and avoid subtotal tumor resection due to intraoperative bleeding. Long follow-up period is important in order to avoid recurrences. Insufficient coverage of this problem in the literature is associated with a low percentage of its occurrence in otosurgical practice, which complicates the timely diagnosis and treatment of this type of tumors of the temporal bone, worsens the prognosis.

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Endolymphatic sac tumour (ELST). of a rare tumour of the temporal bone, presenting as a mass in a cerebello-pontine angle

Cited by 5 publications

References 30 publications

Endolymphatic sac tumor at the cerebellopontine angle: A case report and review of literature

Endolymphatic sac tumor at the cerebellopontine angle: A case report and review of literature

Atypical bilateral cerebellopontine angle medulloblastoma: differential diagnosis, immunohistochemical features and radiological presentation

Endolymphatic sac tumor: rewiev of literature

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