Echocardiographic and angiographic findings in superior-inferior cardiac ventricles

Hery, Eric; Jimenez, Maria; Didier, Dominique; Doesburg, Nicolaas H. van; Guérin, Renée; Fouron, Jean‐Claude; Davignon, A

doi:10.1016/0002-9149(89)91053-9

Cited by 29 publications

(19 citation statements)

References 10 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…1 Almost always, superior-inferior ventricles are associated with cardiovascular pathol-ogy such as discordant atrioventricular connections, ventricular septal defects, straddling atrioventricular valves, ventricular hypoplasia, obstruction of the ventricular outflow tracts, and abnormal ventriculoarterial connections. [2][3][4][5][6][7][8] Due to the complexity of these anomalies, a biventricular repair is often not possible, or else is achieved only after extensive surgery. 7 In their Angiographic Textbooks of Congenital Heart Disease, Freedom and colleagues reported three unrelated children with yet another form of superior-inferior ventricles, which they named ''topsy turvy hearts''.…”

mentioning

confidence: 99%

Prenatal diagnosis of topsy-turvy heart

et al. 2008

View full text Add to dashboard Cite

We describe two siblings of consanguineous parents with a prenatal diagnosis of a currently unique form of congenital cardiac disease characterized by superior-inferior atrial and ventricular arrangement, concordant atrioventricular and ventriculo-arterial connections with normal arterial relationships, and a bizarre topography of the ventricular outlets, with the arterial poles being displaced posterior-inferiorly within the thorax. The abnormally low position of the aortic arch resulted in elongation and stretching of the airways, with severe compression of the trachea and left main bronchus in the surviving sibling. The finding of the same rare abnormality in a son and a daughter born to consanguineous parents supports a single gene disorder with a recessive mode of inheritance.

show abstract

mentioning

confidence: 99%

Prenatal diagnosis of topsy-turvy heart

et al. 2008

View full text Add to dashboard Cite

show abstract

“…Though twisted atrioventricular connections and supero-inferior ventricles frequently coexist, both of these can be found in isolation and are not synonymous. 3 Our study showed supero-inferior ven- Twisted atrioventricular connections can occur even in doubleinlet ventricles when the axes of the two atrioventricular valves cross each other. 11,12 This was seen in 3 of the 12 patients.…”

Section: Aorta and Pulmonary Arterymentioning

confidence: 54%

Imaging characteristics and associations in twisted atrioventricular connections on multidetector computed tomography angiography

Sinha

Pandey

Sharma

et al. 2020

Journal of Cardiac Surgery

View full text Add to dashboard Cite

Aim: To evaluate the imaging characteristics and associations in patients with twisted atrioventricular connections on multidetector computed tomography (CT) angiography. Material and Methods: We retrospectively reviewed 2605 CT angiography studies performed for suspected congenital heart diseases in our institution from January 2014 to December 2018. Twisted atrioventricular connections were diagnosed in 12 patients. Segmental sequential approach developed by Anderson et al was employed to characterize the complex congenital heart disease. Ventricular topology was also determined. CTA was also assessed to look for any associated intra-and extracardiac anomalies. Results: Out of 12 patients with twisted atrioventricular connections, usual visceroatrial arrangement was seen in nine patients, two patients had mirror-imaged viscero-atrial arrangement and one patient had mirror-imaged atrial arrangement. Right-sided heart was seen in four patients. Two patients had discordant atrioventricular connections, seven had concordant atrioventricular connections while three showed double-inlet right ventricle. Ventriculoarterial connections were concordant in two patients, discordant in one patient while nine patients had double-outlet right ventricle. Superior-inferior ventricular morphology with near-horizontal interventricular septum was seen in four patients. Left-sided aortic arch with normal branching pattern was observed in nine patients. No coronary anomaly was seen in any patient. Other associations included ventricular and atrial septal defects, pulmonic stenosis, hypoplasia/atresia of tricuspid valve, straddling of mitral valve, and duplicated superior caval veins. Conclusion: CT angiography is useful in diagnosis of twisted atrioventricular connections with accurate identification of viscero-atrial arrangement, atrioventricular and ventriculoarterial connections, and orientation and presence or absence of associated anomalies.

show abstract

“…This congenital defect was first described by Lev and Rowlatt in 1961, but it was only in 1974 that Anderson et al first used the term crisscross heart. A total of 316 cases of the anomaly have been reported in articles cited in PubMed to date (2016) …”

Section: Discussionmentioning

confidence: 99%

“…Most patients have VSDs, transposition of the great arteries, double‐outlet right ventricle, hypoplastic right ventricle, PS and tricuspid hypoplasia, the latter present in most patients. Other associated defects, although less frequent, are straddling mitral or tricuspid valves, subaortic stenosis, aortic arch obstruction, and mitral stenosis . Anomalies of the coronary circulation may be present and are usually related to the ventricular position, and in these cases, magnetic resonance image (MRI) and angiography are useful tools in the diagnosis and approach .…”

Section: Discussionmentioning

confidence: 99%

Crisscross heart-Morphology, clinical diagnosis, and management options

2016

View full text Add to dashboard Cite

Crisscross heart is a rare cardiac malformation characterized by crossing of the inflow streams of the two ventricles due to a twisting of the heart about its long axis. The developmental mechanisms and causes of crisscross heart remain unknown. Neonates present with cyanosis and a systolic murmur. In this study, we report a case of crisscross heart with situs inversus, concordant atrioventricular and ventriculo arterial connection with ventricular septal defect and pulmonary stenosis, and review the literature on this rare cardiac malformation.

show abstract

Echocardiographic and angiographic findings in superior-inferior cardiac ventricles

Cited by 29 publications

References 10 publications

Prenatal diagnosis of topsy-turvy heart

Prenatal diagnosis of topsy-turvy heart

Imaging characteristics and associations in twisted atrioventricular connections on multidetector computed tomography angiography

Crisscross heart-Morphology, clinical diagnosis, and management options

Contact Info

Product

Resources

About