Duodenal plexiform fibromyxoma: A case report

Lu, Shanyu; Guo, Li

doi:10.1016/j.asjsur.2022.05.150

Cited by 3 publications

(2 citation statements)

References 3 publications

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“…Among the reported cases in the literature, the majority originate in the gastric antrum, affecting young adults, while intestinal origin is much less frequent. 4,5 The case we present can be considered exceptional for 2 reasons: it is a jejunal tumor and it is the youngest patient reported so far.…”

Section: Discussionmentioning

confidence: 83%

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Pediatric Plexiform Fibromyxoma: A Case Report

Bugeda Gómez,

Costa-Roig,

Montecino Romanini

et al. 2024

Journal of Pediatric Hematology/Oncology

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The plexiform fibromyxoma is a rare mesenchymal tumor in adults that generally originates in the antrum of stomach, being its occurrence in pediatric patients exceptional. It was classified as a distinct entity by World Health Organization in 2010. No recurrences and metastases have been documented in many of the reported patients to date, being the surgical treatment curative. We report the case of a 3-month-old infant who presented to the emergency department with an episode of intestinal subocclusion requiring an emergent surgery. During the surgical intervention, a mass was identified in the jejunum, causing partial occlusion of its lumen. The surgical pathology report revealed an infiltrative tumor composed of spindle-shaped cells disposed in a stroma with a plexiform pattern alternating myxoid areas. These findings and the immunohistochemical characteristics of the neoplastic cells led to classify the tumor as a plexiform fibromyxoma. A description of the immunophenotype of this tumor is made and differential diagnosis with other gastrointestinal tumors is also discussed.

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Section: Discussionmentioning

confidence: 83%

“…2 It generally occurs in adults of varying ages, with the most common location being the gastric antrum. However, other origins have been reported, such as the esophagus, 3 duodenum, 4 jejunum, 5 colon, 6 and gallbladder. This tumor is exceptionally rare in pediatric patients.…”

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confidence: 99%