Double outlet right ventricle with discordant atrioventricular connexion: an angiographic analysis of 19 cases

Battistessa, Sergio A.; Soto, Benigno

doi:10.1016/0167-5273(90)90167-4

Cited by 13 publications

(4 citation statements)

References 8 publications

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“…The echocardiogram with Doppler interrogation identifies two noninverted ventricles with left ventricular origin of both great arteries and establishes the location of the ventricular septal defect, and the presence and degree of pulmonary stenosis [8,20]. Double outlet left ventricle is distinguished from origin of both great arteries from an inverted morphologic right ventricle [21].…”

Section: Discussionmentioning

confidence: 99%

Transthoracic echocardiography evaluation of double outlet left ventricle: Unique case report and review of literature

Akhil Mehrotra,

Faiz Illahi Siddiqui,

Ujala Shakya

et al. 2024

World J. Bio. Pharm. Health Sci.

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Double-outlet left ventricle (DOLV) is a rare cardiac malformation in which both great arteries originate from the morphological left ventricle. DOLV is associated with high mortality, generally due to heart failure, myocardial infarction, or aortic thrombosis. With surgery, the 5-year survival rate is estimated at 70%–75%. Most patients will continue to present with residual cardiac anomalies, such as aortic or mitral valve regurgitation, arrhythmias, or hypertension. We are reporting a complex case of cyanotic congenital heart disease in a 5 month old female infant suffering from DOLV, who presented to us with recurrent chest infections and bluish colouration of skin.

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Section: Discussionmentioning

confidence: 99%

Transthoracic echocardiography evaluation of double outlet left ventricle: Unique case report and review of literature

Akhil Mehrotra,

Faiz Illahi Siddiqui,

Ujala Shakya

et al. 2024

World J. Bio. Pharm. Health Sci.

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“…This congenital defect was first described by Lev and Rowlatt in 1961, but it was only in 1974 that Anderson et al first used the term crisscross heart. A total of 316 cases of the anomaly have been reported in articles cited in PubMed to date (2016) …”

Section: Discussionmentioning

confidence: 99%

“…Most patients have VSDs, transposition of the great arteries, double‐outlet right ventricle, hypoplastic right ventricle, PS and tricuspid hypoplasia, the latter present in most patients. Other associated defects, although less frequent, are straddling mitral or tricuspid valves, subaortic stenosis, aortic arch obstruction, and mitral stenosis . Anomalies of the coronary circulation may be present and are usually related to the ventricular position, and in these cases, magnetic resonance image (MRI) and angiography are useful tools in the diagnosis and approach .…”

Section: Discussionmentioning

confidence: 99%

Crisscross heart-Morphology, clinical diagnosis, and management options

2016

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Crisscross heart is a rare cardiac malformation characterized by crossing of the inflow streams of the two ventricles due to a twisting of the heart about its long axis. The developmental mechanisms and causes of crisscross heart remain unknown. Neonates present with cyanosis and a systolic murmur. In this study, we report a case of crisscross heart with situs inversus, concordant atrioventricular and ventriculo arterial connection with ventricular septal defect and pulmonary stenosis, and review the literature on this rare cardiac malformation.

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“…Atrioventricular discordance is a rare congenital heart disease, as it accounts for less than 1% of all of them [1]. It has been described that approximately 15% of the cases of atrioventricular discordance may also present with double outlet of the morphological right ventricle [2]. Several studies suggest a genetic predisposition as the main cause of congenital heart disease; the heterozygous ISL1 mutation (gene related with heart development transcription factors) was studied on 114 patients with congenital heart disease and compared with a control group of 218 subjects.…”

Section: Introductionmentioning

confidence: 99%

Granulicatella adiacens endocarditis of a complex congenital heart disease on an adult

Espínola‐Zavaleta¹,

Castellanos-Vizcaíno²,

Salazar-Vitale³

et al. 2019

Clin Res Trial

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We present a 23-year-old man with complex CHD, who came to our institution due to moderate exertion dyspnea and fever. He was diagnosed with mitral valve endocarditis and Granulicatella adiacens was isolated. He was treated with antibiotics and discharged as he refused surgery. He came back on August 2019 with progressive increase of abdominal perimeter, lower limbs edema and chest pain. On cardiac examination pericardial rub and III/VI apical holosystolic murmur were found. The transthoracic echocardiogram showed situs solitus, atrioventricular discordance, double-outlet right ventricle with transposition of great arteries, interventricular septal defect, moderate tricuspid regurgitation, vegetations in both leaflets of mitral valve and severe mitral regurgitation, subvalvular pulmonary stenosis and huge pericardial effusion. The patient underwent successful mitral valve replacement and he was discharged in good condition.

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Double outlet right ventricle with discordant atrioventricular connexion: an angiographic analysis of 19 cases

Cited by 13 publications

References 8 publications

Transthoracic echocardiography evaluation of double outlet left ventricle: Unique case report and review of literature

Transthoracic echocardiography evaluation of double outlet left ventricle: Unique case report and review of literature

Crisscross heart-Morphology, clinical diagnosis, and management options

Granulicatella adiacens endocarditis of a complex congenital heart disease on an adult

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