Double-Outlet Right Ventricle

Freedom, Robert M.; Smallhorn, Jeffrey

doi:10.1007/978-1-4471-1814-5_27

Cited by 5 publications

(3 citation statements)

References 82 publications

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“…The VSD in DORV approximates the subpulmonary infundibulum although the infundibulum itself does not override the ventricular septum so that, strictly speaking, the defect is not subpulmonary but rather juxtapulmonary ( Fig. 1-a) Freedom et al (1997). In the Taussig-Bing defect (Taussig and Bing, 1949), a variant of DORV, the infundibular septum (septal end/ conus ridge 1) fuses posteriorly with the ventricular septum near the right posterior division of the SMT.…”

Section: Dorv Versus Ad Defectsmentioning

confidence: 99%

Double Outlet Right Ventricle Versus Aortic Dextroposition: Morphologically Distinct Defects

Restivo

Unolt

Putotto

et al. 2013

The Anatomical Record

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This study concerns the morphological differentiation between double outlet right ventricle (DORV) and aortic dextroposition (AD) defects, namely tetralogy of Fallot and Eisenmenger anomaly. Indeed, despite the similar condition in terms of sequential ventriculo-arterial connections, DORV and AD are two distinct morphological entities. It is proposed that the borderline between these two groups of malformations is represented by the specific insertion of the infundibular septum into the left anterior cranial division of the septomarginal trabeculation (or septal band) occurring in ADs and lacking in DORV. Furthermore, the spiraliform versus straight parallel arrangement of the great arteries in the two groups of anomalies is emphasized as an additional and distinctive morphological feature. Emphasis is also given to the association of straight parallel great arteries conotruncal malformations, DORV and transposition of the great arteries, with the asplenia type of heterotaxy laterality defects. Within this context, the absence of subaortic ventricular septal defect and concomitantly of spiraliform great arteries in the asplenia group of heterotaxy anomalies, as detected by this study, further substantiates our belief of not mixing collectively the ADs with the DORV in clinico-pathological diagnosis.

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Section: Dorv Versus Ad Defectsmentioning

confidence: 99%

Double Outlet Right Ventricle Versus Aortic Dextroposition: Morphologically Distinct Defects

Restivo

Unolt

Putotto

et al. 2013

The Anatomical Record

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“…Echocardiography is now the technique used most frequently in evaluating the anatomy, haemodynamics, and function of the heart prior to and after surgical repair or palliation. 6,7 Currently, it is the most reliable means of establishing the diagnosis of double outlet from the right ventricle, albeit that this could well change as more units gain access to techniques producing tomographic images that permit the relationship of the circumferences of the arterial valve to be established relative to the crest of the muscular septum. It is still in the assignment of overriding arterial valves that most difficulties are encountered with making the diagnosis of double outlet, and three-dimensional echocardiography is also likely to provide significant added value when making such adjudications.…”

Section: The Left Ventricular Outflow Tract In Double Outlet Right Vementioning

confidence: 99%

Echocardiographic assessment of the aortic valve and left ventricular outflow tract

Asante‐Korang

Anderson

2005

Cardiol Young

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The previous reviews in this section of our Supplement1,2 have summarized the anatomic components of the ventriculo-arterial junctions, and then assessed the echocardiographic approach to the ventriculo-arterial junction or junctions as seen in the morphologically right ventricle. In this complementary review, we discuss the echocardiographic assessment of the comparable components found in the morphologically left ventricle, specifically the outflow tract and the arterial root. We will address the echocardiographic anatomy of the aortic valvar complex, and we will review the causes of congenital arterial valvar stenosis, using the aortic valve as our example. We will also review the various lesions that, in the outflow of the morphologically left ventricle, can produce subvalvar and supravalvar stenosis. We will then consider the salient features of the left ventricular outflow tract in patients with discordant ventriculo-arterial connections, and double outlet ventricles. To conclude the review, we will briefly address some rarer anomalies that involve the left ventricular outflow tract, showing how the transesophageal echocardiogram is used to assist the surgeon preparing for repair. The essence of the approach will be to consider the malformations as seen at valvar, subvalvar, or supravalvar levels,1 but we should not lose sight of the fact that aortic coarctation or interruption, hypoplasia of the left heart, and malformations of the mitral valve are all part of the spectrum of lesions associated with obstruction to the left ventricular outflow tract. These additional malformations, however, are beyond the scope of this review.

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“…Five groups of DORV have been described in the medical literature [1][2][3] , based on the spatial relationship between the great arteries ( fig. 2): a) posterior and rightsided aorta (normal relation); b) aorta and pulmonary trunk located side by side; c) anterior and right-sided aorta; d) anterior aorta; and e) anterior and left-sided aorta.…”

mentioning

confidence: 99%

Double outlet right ventricle with anterior and left-sided aorta and subpulmonary ventricular septal defect

Peixoto¹,

Leal²,

Silva³

et al. 1999

Arq. Bras. Cardiol.

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Double outlet right ventricle (DORV) is a heterogeneous group of abnormal ventriculoarterial connections where, by definition, both great arteries (pulmonary artery and aorta) arise primarily from the morphologically right ventricle. This condition affects 1-1.5% of the patients with congenital heart diseases, with a frequency of 1 in each 10,000 live births. We report the case of an 18-day-old infant with DORV and extremely rare anatomical features, such as anterior and left-sided aorta and subpulmonary ventricular septal defect (VSD). In addition to the anatomic features, the role of the echocardiogram for guiding the diagnosis and the surgical therapy of this congenital heart disease are discussed.

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Double-Outlet Right Ventricle

Cited by 5 publications

References 82 publications

Double Outlet Right Ventricle Versus Aortic Dextroposition: Morphologically Distinct Defects

Double Outlet Right Ventricle Versus Aortic Dextroposition: Morphologically Distinct Defects

Echocardiographic assessment of the aortic valve and left ventricular outflow tract

Double outlet right ventricle with anterior and left-sided aorta and subpulmonary ventricular septal defect

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