Double incomplete aortic arch and Kommerell's Diverticulum as a cause of chronic cough

Abstract

Vascular rings which can cause symptoms related the trachea and esophagus compression occur in less than 1% of all cardiovascular malformations. Double incomplete aortic arch with right-sided aorta and aberrant left subclavian artery is the rarest one, and its present in 0.04-0.1% of autopsy series. A case of this malformation with a Kommerell's Diverticulum is presented. This diverticulum has risk of severe complications such as dissection and/or rupture.

Double Aortic Arch With Kommerell Diverticulum

“…Much less commonly they are associated with a double aortic arch. We could only find two case reports of double aortic arch with KD [7,8]. To our knowledge, this is the first study of its kind to characterize the presenting symptoms, operative management, and postoperative outcomes of a series of patients with both double aortic arch and KD.…”

“…In the current era, if the patient has a KD, we now know that in most cases this should be addressed by resecting the KD and transferring the left subclavian artery to the left carotid artery [4][5][6]. Currently, there are only case reports on the management of patients with a KD in the setting of a double aortic arch [7,8]. The objective of this study was to examine the patient demographics and presenting symptoms in a series of patients with double aortic arch and KD and to determine the results of KD excision in this patient population.…”

Congenital arch malformation: a review of morphology and surgical management of circumflex aortic arch

“…Following repair of double aortic arch where the smaller left arch is divided [ Figure 3A-C], the preserved retroesophageal arch segment will resemble a circumflex arch [35] . A completely atretic segment [ Figure 3D] can be present between the left common carotid and subclavian arteries in the setting of a double aortic arch with a dominant right [36][37][38] . They are strictly speaking, by morphology criteria, a double aortic arch, but functionally resemble a circumflex arch with a high retroesophageal segment above the tracheal carina [36] .…”

Aberrant right subclavian artery aneurysm: A rare entity

“…This diverticulum may cause pressure on the tracheoesophageal region, leading to dissection/rupture due to excessive widening. [3,4] Herein, we present an 80-year-old male patient with an ARSA aneurysm.…”