Disorders of Nails

Pachyonychia congenita is a rare type of ectodermal dysplasia further classified into 4 types. Cutaneous manifestations seen in most of the cases of Pachyonychia congenita include palmoplantar keratoderma, follicular hyperkeratosis, wedge shaped nails, oral leukokeratosis and woolly hair. A 25-year-old male presented to us with thickened nails and scanty scalp hair. On examination, we noticed hyperkeratotic plaques over both the soles, palmoplantar hyperhidrosis and yellowish discoloration, wedging with subungual hyperkeratosis of all the nails. Follicular hyperkeratotic papules and steatocystoma multiplex were also observed over the scalp and face. The patient had history of natal teeth and on dental examination, lower central incisors were absent. All cutaneous changes in our case had manifested first in the 2nd decade except for natal teeth. All the above features suggested the diagnosis of pachyonychia congenita with late onset (PC tarda), which is an infrequently reported rare variant.

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“…[ 5 6 ] Pachyonychia congenita tarda is a rare variant with onset later in life ranging from the second decade to middle age. [ 7 ]…”

Section: Discussionmentioning

confidence: 99%

Pachyonychia congenita with late onset (PC tarda)

Sravanthi

Srivalli

Gopal

et al. 2016

Indian Dermatol Online J

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“…At present, the definition of nail matrix is controversial 18,19 . The matrix can be subdivided into dorsal, intermediate, and ventral (nail bed) sections, but the role of the nail bed in the production of the nail remains unclear 20 . Johnson and colleagues 21 measured thickness and mass weight (mg/cm 2 ) of the normal nail; their findings indicated that the nail plate may thicken by as much as 20% as it passes from the distal margin of the lunula to the end of the nail.…”

Section: Discussionmentioning

confidence: 99%

Morphologic Study of Normal, Ingrown, and Pincer Nails

Kosaka

Kusuhara

Mochizuki

et al. 2010

Dermatologic Surgery

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“…It should be considered in children who suck their thumbs leading to viral autoinoculation, healthcare providers, as well as following genital herpes exposure. [ 15 20 ] Incision and drainage are contraindicated and tzanck smear and/or culture are pivotal in diagnosis. [ 2 5 , 15 ]…”

Section: A Cute P Aronychiamentioning

confidence: 99%

Acute and chronic paronychia revisited: A narrative review

Relhan¹,

Bansal²

2022

J Cutan Aesthet Surg

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Paronychia refers to the inflammation of the tissue which immediately surrounds the nail and it can be acute (<6 weeks duration) or chronic (>6 weeks duration). Disruption of the protective barrier between the nail plate and the adjacent nail fold preceded by infectious or noninfectious etiologies results in the development of paronychia. A combination of general protective measures, and medical and/or surgical interventions are required for management. This review explores the pathogenesis, clinical features, differential diagnosis, medical, and surgical management of paronychia. For the purpose of this review, we searched the PubMed, Cochrane, and Scopus databases using the following keywords, titles, and medical subject headings (MeSH): acute paronychia, chronic paronychia, and paronychial surgeries. Relevant review articles, original articles, and case reports/series published till February 2020 were included in this study.

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Disorders of Nails

Cited by 23 publications

References 592 publications

Pachyonychia congenita with late onset (PC tarda)

Pachyonychia congenita with late onset (PC tarda)

Morphologic Study of Normal, Ingrown, and Pincer Nails

Acute and chronic paronychia revisited: A narrative review

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