Özet-İki yaşında iki yönlü Glenn ameliyatı geçirmiş ve beş yaşında pulmoner trunkus bağlanması ve kalp dışı Fontan ameliyatı geçirmiş çift çıkımlı sağ ventrikül, ventriküler septal defekt ve pulmoner stenozlu bir hasta sunduk. Hasta Fontan ameliyatından üç ay sonra plevra sıvısıyla başvurdu. Fizik muayenesinde pulmoner odakta 3/6 sistolik üfürüm duyuldu. Ekokardiyografik değerlendirimede pulmoner öne doğru akım ve burada 80 mmHg basınç farkı tespit edildi. Kalp kateterizasyonu ve anjiyografi ça-tallanma düzeyinde darlık ve pulmoner öne doğru akımı gösterdi. Her iki patolojiyi de transkateter yolla kaplı stent yerleştirerek giderdik. Kontrol anjiyogramında çatallanma düzeyinde darlığın giderildiği ve öne doğru akımın kaybolduğu izlendi.Summary-A 5-year-old male with a double outlet right ventricle with noncommitted ventricular septal defect and pulmonary stenosis underwent a bidirectional Glenn operation at 2 years and a Fontan operation with ligation of the pulmonary trunk at 5 years. He presented with pleural effusion 3 months after the Fontan operation. Physical examination revealed a grade 3/6 systolic murmur in the pulmonary area. Echocardiographic evaluation revealed an antegrade pulmonary flow (APF) of gradient 80 mmHg across the ventriculopulmonary communication. Cardiac catheterization and angiography demonstrated the presence of residual antegrade pulmonary flow and stenosis at the pulmonary artery bifurcation. Both pathologies were treated using a single covered stent. Relief of the pulmonary artery stenosis and total occlusion of the residual APF was demonstrated on a control angiogram.
256F ontan surgery is the final stage operation of a series of palliative operations. It is performed on patients with complex congenital heart disease who are not suitable for biventricular repair. The procedure diverts systemic venous blood returning to the right atrium via the inferior vena cava to the pulmonary arteries. Since blood is transmitted passively to the lungs in Fontan circulation, pulmonary artery size, preoperative pulmonary arterial pressure, pulmonary vascular resistance, and the presence of branched pulmonary artery stenosis are of great importance, and determine the outcome of the procedure in these patients. Even a minor increase in pulmonary arterial pressure or an alteration in pulmonary blood flow may affect the hemodynamics of circulation and result in complications such as pleural effusion, ascites, or protein losing enteropathy. [1,2] This report describes successful transcatheter treatment using a single covered stent of a pleural effusion from pulmonary artery stenosis and residual pulmonary antegrade flow in a 5-year-old male with Fontan circulation.
CASE REPORTA 5-year-old male presented with pleural effusion 3 months after an extracardiac conduit Fontan operation. His initial diagnosis was double outlet right ventricle with noncommited ventricular septal defect and pulmonary stenosis. The patient had undergone a bidirectional Glenn operation at 2 years and an extracardiac conduit Fontan...