Development of an Evaluation Scale for Sitting and Standing From the Ground for Children With Duchenne Muscular Dystrophy

Abstract

The authors developed an evaluation scale for sit-stand from the ground for children with Duchenne muscular dystrophy (DMD) and tested its reliability. The construction occurred in stages: (a) the characterization of the movement in healthy children, (b) the characterization of the movement in children with DMD, (c) the elaboration of the 1st version of the scale and the manual, (d) the evaluation by experts and readjustments, and (e) the analysis of inter- and intraexaminer reliability and correlation with the Vignos Scale, age, and time for the execution of the activity. The scale comprehended 3 phases for sitting and 5 for the standing. A very good repeatability of the measures of sitting and standing (ICC = 0.89 and 0.84, respectively) and excellent reproducibility (ICC = 0.93 and 0.92, respectively) was demonstrated. The Kappa coefficient for the 8 phases in the interexaminer analysis varied from 0.77 to 1.00 (excellent reliability), and in the intraexaminer analysis varied from 0.80 to 1.00 (excellent reliability). Good correlation was found between the variables on the Vignos Scale (age: r = 0.58; stand: r = 0.56). The scale is a reliability instrument that allows evaluation of the activity of sitting and standing in children with DMD.

How often should sitting and rising from a chair be evaluated in patients with Duchenne muscular dystrophy?

“…The FES-DMD has four domains: sitting and rising from a chair 7 ; walking 8 ; climbing up and down steps 9 ; and sitting down on, and standing up from the floor 10 . Excellent intra-and interrater reliabilities of all domains have been demonstrated 7,8,9,10 . In the FES-DMD, the tasks are videoed, which reduces evaluation time and patient fatigue (caused by the repetition of the activities).…”

Compensatory movements during functional activities in ambulatory children with Duchenne muscular dystrophy

“…Previous research assessed the reliability and validity of two domains (sitting down on the floor/rising from the floor and climbing up/down steps) of the Functional Evaluation Scale for ambu latory patients with DMD (FES-DMD) 7,8 . These studies pro vided a scale for the systematized observation of movements of children with DMD.…”

Criação e análise de confiabilidade de escala de avaliação funcional da marcha para crianças com Distrofia Muscular de Duchenne

“…Possíveis pontuações nesta fase variam de 0 a 13 (Quadro 3). (Hukuda et al, 2013;Escorcio et al, 2011;Fernandes et al, 2010). …”

“…A FES-DMD é composta por quatro domínios, a saber, sentar e levantar da cadeira (Hukuda et al, 2013), sentar e levantar do chão (Escorcio et al, 2011), subir e descer escadas (Fernandes et al, 2010) …”