The authors aimed to (a) develop a scale to evaluate non-wheelchair-dependent children with Duchenne muscular dystrophy (DMD) while sitting and standing from the chair, (b) test its reliability, and (c) correlate the scores of this scale with the time, the age and the Vignos. Thirty DMD boys performed sit-to-stand and stand-to-sit from the chair 4 times. Scale development was based on a previous movement characterization in healthy children and in DMD children and on suggestions by physical therapists with expertise in DMD. The final version of the scale was submitted to the analysis of reliability. The sitting evaluation consists of phases: flexion, contact of the hip with the chair, extension. The standing evaluation comprehends the phases: flexion; transference; extension. Sitting and standing phases presented an excellent reliability (intraclass correlation coefficient [ICC] ≥ 0.91) and a good reproducibility (ICC ≥ 0.89). The scores generated by sitting on the chair correlated to the time taken to perform the tasks (r = .69) and to the age of the patient (r = .44) and the score of standing from the chair also correlated to the time of performance (r = .66). The sit-to-stand functional evaluation scale DMD is a reliable assessment tool that allows the description and quantification of the functional performance of DMD children.
Objective: To determine how often sitting/rising from a chair should be assessed in Duchenne muscular dystrophy (DMD) patients to avoid redundant/missing data. Methods: Sitting/rising from a chair was evaluated in 26 DMD children (5-12 yrs), in three-month intervals, over twelve months, with the Functional Evaluation Scale (domain sitting/rising from a chair). Scores were compared by effect sizes (ES) and standardized response means (SRM) (responsiveness analysis). Results: Sit-to-stand showed low-to-moderate responsiveness in three-month intervals
BACKGROUND: Knowing the potential for and limitations of information generated using different
evaluation instruments favors the development of more accurate functional
diagnoses and therapeutic decision-making. OBJECTIVE: To investigate the relationship between the number of compensatory movements when
climbing up and going down stairs, age, functional classification and time taken
to perform a tested activity (TA) of going up and down stairs in boys with
Duchenne muscular dystrophy (DMD). METHOD: A bank of movies featuring 30 boys with DMD performing functional activities was
evaluated. Compensatory movements were assessed using the climbing up and going
down stairs domain of the Functional Evaluation Scale for Duchenne Muscular
Dystrophy (FES-DMD); age in years; functional classification using the Vignos
Scale (VS), and TA using a timer. Statistical analyses were performed using the
Spearman correlation test. RESULTS: There is a moderate relationship between the climbing up stairs domain of the
FES-DMD and age (r=0.53, p=0.004) and strong relationships with VS (r=0.72,
p=0.001) and TA for this task (r=0.83, p<0.001). There were weak relationships
between the going down stairs domain of the FES-DMD-going down stairs with age
(r=0.40, p=0.032), VS (r=0.65, p=0.002) and TA for this task (r=0.40, p=0.034).
CONCLUSION: These findings indicate that the evaluation of compensatory movements used when
climbing up stairs can provide more relevant information about the evolution of
the disease, although the activity of going down stairs should be investigated,
with the aim of enriching guidance and strengthening accident prevention. Data
from the FES-DMD, age, VS and TA can be used in a complementary way to formulate
functional diagnoses. Longitudinal studies and with broader age groups may
supplement this information.
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