Desmoid-type Fibromatosis of the Mesentery: A Case Report

Abstract

SummaryDesmoid-type bromatosis is a rare mesenchymal neoplasm with locally aggressive, in ltrating and destructive growth that is not characterized by a metastatic potential. According to their anatomical position, desmoid-type bromatoses can be divided into three groups: extraabdominal, intra-abdominal, and bromatoses of the abdominal wall. Mesenteric bromatoses account for 8% of the intra-abdominal ones. The latter are characterized by myo broblastic proliferation and in ltration of both the pelvic and abdominal organs. We report a 26-year-old woman who complained of abdominal enlargement, feeling of heaviness, discomfort and re ux, which symptoms dated back 1-2 months prior to hospitalization. The patient underwent laparotomy due to subocclusive symptoms. Intraoperatively, a tumor sized 30 cm in diameter was found. The tumor originated from the mesentery and in ltrated in the jejunum, the entire ileum, and part of the caecum with perforation towards the abdominal cavity. The histological and immun histochemical examinations are important for clari cation of the diagnosis. The treatment requires a multidisciplinary approach, in which the surgical method has the key role.