2010
DOI: 10.1590/s0004-28032010000400010
| View full text |Cite
|
Sign up to set email alerts
|

Abstract: -Context -Desmoid tumors constitute one of the most important extraintestinal manifestations of familial adenomatous polyposis. The development of desmoids is responsible for increasing morbidity and mortality rates in cases of familial adenomatous polyposis. Objectives -To evaluate the occurrence of desmoid tumors in familial adenomatous polyposis cases following prophylactic colectomy and to present patient outcome. Methods -Between 1984 and 2008, 68 patients underwent colectomy for familial adenomatous poly… Show more

Help me understand this report

Search citation statements

Order By: Relevance

Paper Sections

Select...
5

Citation Types

0
17
0

Year Published

2013
2013
2022
2022

Publication Types

Select...
5
2

Relationship

1
6

Authors

Journals

citations
Cited by 21 publications
(17 citation statements)
references
References 31 publications
0
17
0
Order By: Relevance
“…The etiology of DT is still unclear. Approximately 2% of DT are associated with FAP caused by mutation in the FAP gene that is located in chromosome 5q21, or Gardner's syndrome [11,12]. Known risk factors associated with DT are as follows: prior abdominal surgery, typically prophylactic colectomy, localization of the FAP germline mutation, female sex, and a family history of DT [13].…”
Section: Discussionmentioning
confidence: 99%
“…The etiology of DT is still unclear. Approximately 2% of DT are associated with FAP caused by mutation in the FAP gene that is located in chromosome 5q21, or Gardner's syndrome [11,12]. Known risk factors associated with DT are as follows: prior abdominal surgery, typically prophylactic colectomy, localization of the FAP germline mutation, female sex, and a family history of DT [13].…”
Section: Discussionmentioning
confidence: 99%
“…Desmoid tumours are rare fibromatous lesions that are non-metastasising but locally aggressive and have a high rate of recurrence even after complete resection [1], [2] These slow-growing tumours commonly arise in the abdominal wall or in the intra-abdominal region.…”
Section: Discussionmentioning
confidence: 99%
“…2% of cases of desmoid tumours are associated with FAP [1]. Whereas the incidence of desmoid tumours in the general population is 2–4 per million per year, the incidence in FAP is 10–20%, meaning that a patient with FAP is at an 852-fold increased risk of developing a desmoid tumours [2], [3], [6].…”
Section: Discussionmentioning
confidence: 99%
See 2 more Smart Citations