Dermatofibrosarcoma non‐protuberans: Description and report of five cases of a morpheaform variant of dermatofibrosarcoma

Wc, Lambert; Abramovits, William; Gonzalez-Sevra, A; Souchon, Eduardo; Ra, Schwartz; Wp, Little

doi:10.1002/jso.2930280104

Cited by 53 publications

(40 citation statements)

References 16 publications

(27 reference statements)

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“…In 1985, Lambert et al [2] reported 5 cases of dermatofibrosarcoma in which the tendency to depress beneath the surface of the skin was observed. Clinically, they resembled morphea or morphea-form basal cell carcinoma but showed typical DFSP histologically.…”

Section: Discussionmentioning

confidence: 99%

“…We report a patient with the atrophic variant of DFSP and review the literature [2, 3, 7, 8, 9, 10, 11] to clarify the clinical characteristics of this variant.…”

Section: Introductionmentioning

confidence: 99%

“…It occurs in both sexes over a wide range of ages and tends to involve the trunk and proximal extremities [1, 2]. Although DFSP has a low metastatic potential, it has been known to recur frequently after surgery [1].…”

Section: Introductionmentioning

confidence: 99%

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Atrophic Dermatofibrosarcoma protuberans: A Case Report and Review of the Literature

et al. 1998

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Dermatofibrosarcoma protuberans is not a difficult tumor to recognize because of its characteristic clinical appearance, although some unusual variants have been reported. We describe the atrophic variant of dermatofibrosarcoma protuberans in a 21-year-old female. The lesion was a smooth-surfaced, oval depression on the left subclavicular area, with a violaceous plaque at the center. The suspected clinical diagnosis did not include fibrous tumors, although histological examination showed the typical picture of dermatofibrosarcoma protuberans. Positive CD34 staining was also helpful in the diagnosis. We review 14 cases of the atrophic variant of dermatofibrosarcoma protuberans in the literature. Dermatologists should be aware of this uncommon but characteristic appearance of atrophic dermatofibrosarcoma protuberans.

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Section: Discussionmentioning

confidence: 99%

“…We report a patient with the atrophic variant of DFSP and review the literature [2, 3, 7, 8, 9, 10, 11] to clarify the clinical characteristics of this variant.…”

Section: Introductionmentioning

confidence: 99%

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Atrophic Dermatofibrosarcoma protuberans: A Case Report and Review of the Literature

et al. 1998

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“…Rarely, the initial plaque may be atrophic or depressed and this atrophic appearance may persist. 3 It has been suggested that "protuberans" could be discarded from the term DFSP altogether, as such lesions often lack the protruding nodules despite advanced growth. Atrophic DFSP, morpheaform variant of DFSP and dermatofibrosarcoma non-protuberans are synonymous terms for this atrophic clinical presentation, with atrophic DFSP being the most adopted.…”

Section: Introductionmentioning

confidence: 99%

“…4 Atrophic DFSP was first reported in 1985. 3 Given the typical "protuberant" morphology of DFSP, such atrophic lesions can be difficult to diagnose clinically. Including our case, there have been 33 reported cases of this variant to date.…”

Section: Introductionmentioning

confidence: 99%

Atrophic dermatofibrosarcoma protuberans

Bakry¹,

Attia²

2012

J Dermatol Case Rep

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Background: Dermatofibrosarcoma protuberans (DFSP) is an uncommon malignant mesenchymal tumor that arises in the dermis and is characterised by latency in its initial detection. As a rare form, atrophic or morphea-like DFSP has been documented. Atrophic DFSP resemble other benign lesions such as morphea, idiopathic atrophoderma, atrophic scar, anetoderma or lipoatrophy. It behaves like classic DFSP. It commonly favours young to middle aged adults. It has a slow infiltrative growth and a high rate of local recurrence if not completely excised. Metastases are rare and occur after repeated local recurrence. Surgical excision is the best line of treatment. Long term follow up is required to detect recurrence. Main observations:We report a case of atrophic DFSP in a 52-year-old female patient. Diagnosis was achieved according to clinical, histopathological and immunohistochemical findings. Tumor was surgically excised with safety margin and the patient is still under follow up.Conclusions: Atrophic DFSP is a rare variant of DFSP. It is a tumor of low to moderate grade malignancy. Surgical excision is the best line of management. Long term follow up is necessary.

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A Localized Atrophic Plaque on the Back

Ashack¹,

Tejada²,

Parker³

et al. 1992

Arch Dermatol

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A 25-year-old white man was referred to the dermatology clinic for evaluation of an asymptomatic, slowly enlarging plaque located on the posterior aspect of his left shoulder. The plaque was first noticed approximately 8 years ago and had been examined by several physicians, who felt the lesion was not of concern; thus, no treatment was rendered.On examination, a 2.5\m=x\1.5-cmfirm, violaceous, slightly depressed lesion was noted superior to the left scapula. Adjacent to this firm area was an atrophic-appearing area of the lesion that was less pigmented and more depressed (Fig 1).A 3-mm punch biopsy specimen was taken from the lesion and is shown in Figs 2 and 3.

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Dermatofibrosarcoma non‐protuberans: Description and report of five cases of a morpheaform variant of dermatofibrosarcoma

Cited by 53 publications

References 16 publications

Atrophic Dermatofibrosarcoma protuberans: A Case Report and Review of the Literature

Atrophic Dermatofibrosarcoma protuberans: A Case Report and Review of the Literature

Atrophic dermatofibrosarcoma protuberans

A Localized Atrophic Plaque on the Back

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