Déjà Vu

Abstract

Sudden cardiac arrest from anomalous coronary artery from the opposite sinus of Valsalva is rarely observed in children under 10 years of age. We report a 7-week-old infant with a brief resolved unexplained event from left anomalous aortic origin of a coronary artery who underwent unroofing and again developed syncope at 8 years of age. Ischemia was detected by stress echocardiography both times. ( Level of Difficulty: Advanced. )

Histopathology of resected tissue from repair of anomalous aortic origin of a coronary artery: Potential mechanism of coronary artery compression

“…Its known association with sudden cardiac death depicts the potential gravity of its clinical consequence. 1 , 2 , 3 , 4 , 5 Most commonly, the right coronary artery arises from the left coronary sinus of Valsalva and takes an interarterial course. 6 Usually, the proximal part of the anomalous coronary artery has an intramural segment coursing within the wall of the aorta before exiting the aortic adventitia.…”