Das adrenogenitale Syndrom im Kindesalter

Bierich, J. R.

doi:10.1007/978-3-642-94722-3_9

Cited by 21 publications

(4 citation statements)

References 137 publications

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“…Already in 1955, Fischer suggested to search for endocrine disorders in case of premature calcifications of the rib cartilages [ 14 ]. Among later reports of diseases associated with premature CCC, there were indeed observations of hyperthyroidism [ 5 , 6 ] or of cases with adrenogenital syndrome [ 8 , 9 ]. The full picture of an adrenogenital syndrome could never be proven in our patients, but some of its symptoms were seen, for example, a partial insufficiency of the suprarenal glands or an increased excretion of androgen metabolites in the urine.…”

Section: Discussionmentioning

confidence: 99%

“…The forms and the onset of these calcifications were used to determine the gender and the age of unknown bodies in the forensic medicine [ 2 – 4 ]; however, the clinical significance of premature calcifications of the lower rib cartilages is not fully elucidated as yet. In case reports, there have been descriptions of an association of premature calcifications with hyperthyroidism [ 5 , 6 ], corticosteroid medication [ 7 ], and rare congenital diseases such as adrenogenital syndrome [ 8 , 9 ] or Keutel syndrome [ 10 , 11 ], but some authors regard even extensive costal cartilage calcifications (CCC) as a normal finding or variant [ 12 ].…”

Section: Introductionmentioning

confidence: 99%

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Premature Calcifications of Costal Cartilages: A New Perspective

Rhomberg

Schuster

2014

Radiology Research and Practice

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Background. Calcifications of the costal cartilages occur, as a rule, not until the age of 30 years. The knowledge of the clinical significance of early and extensive calcifications is still incomplete. Materials and Methods. A search was made to find patients below the age of 30 years who showed distinct calcifications of their lower costal cartilages by viewing 360 random samples of intravenous pyelograms and abdominal plain films. The histories, and clinical and laboratory findings of these patients were analyzed. Results. Nineteen patients fulfilled the criteria of premature calcifications of costal cartilages (CCCs). The patients had in common that they were frequently referred to a hospital and were treated by several medical disciplines. Nevertheless many complaints of the patients remained unsolved. Premature CCCs were often associated with rare endocrine disorders, inborn errors of metabolism, and abnormal hematologic findings. Among the metabolic disorders there were 2 proven porphyrias and 7 patients with a suspected porphyria but with inconclusive laboratory findings. Conclusion. Premature CCCs are unlikely to be a normal variant in skeletal radiology. The findings in this small group of patients call for more intensive studies, especially in regard to the putative role of a porphyria.

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Section: Discussionmentioning

confidence: 99%

Section: Introductionmentioning

confidence: 99%

Premature Calcifications of Costal Cartilages: A New Perspective

Rhomberg

Schuster

2014

Radiology Research and Practice

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“…Bierich propagierte in Bezug auf das AGS das Baltimorer Behandlungsvorgehen inklusive der frühzeitigen Operationen und -anders als Wallis -auch das gender-Konzept, aber er übernahm auch die Konstruktion der psychosexuellen Indifferenz. Indem er diese aber teils als Reaktion auf das uneindeutige körperliche Erscheinungsbild, teils als zerebrale "Störung" aufgrund des Kortisolmangels erklärte, verschob er die Begrün-dungen dermaßen, dass die chirurgischen Eingriffe und die Kortisontherapie geeignet erscheinen mussten, die Indifferenz zu überwinden [Bierich, 1958]. Damit hebelte er obendrein Bleulers Indifferenz-Argument gegen die Verallgemeinerbarkeit der Ergebnisse der Baltimorer Intersexualitätsforschung aus, da diese ja gerade auch an behandelten Intersexuellen gewonnen worden waren, bei denen in Bierichs Sicht die Indifferenz überwunden und damit der "normalen" Entwicklung vergleichbare Voraussetzungen geschaffen worden waren.…”

Section: Psychosexuelle "Indifferenz"unclassified

Die Formierung von gender am “Naturexperiment” Intersexualität in der zweiten Hälfte des 20. Jahrhunderts

Klöppel

2006

N.T.M.

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This paper shows the formation of the psychological concept of gender from the testing of a new intersex treatment in the 1950s. By analyzing the initial refusal and final success of the new concept and guidelines in the German speaking medical community, it points to the decisive role of treating intersexuals as "experiments of nature" for the clinical research in psychosexual development. This new technology brought the divergent problematizations of "ambiguous sex" in line thus bridging the gap between scientific and clinical approaches and providing the material basis for turning gender into a scientific and practical entity.

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“…Other causes can be due to underlying pulmonary infection and costochondral Inflammation 6,7 . Rare congenital diseases such Adrenogenital syndrome 8,9 or Keutel syndrome 10,11 are also associated with costochondral calcification.…”

Section: Introductionmentioning

confidence: 99%

Premature idiopathic costochondral calcification: A Case Report

Kabir

Hossain

Kiang

2017

BJMS

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Calcification of costal cartilage increases with age and it is rare before the age of thirty years. Early onset of costochondral calcification can be associated several endocrine and metabolic diseases, following a trauma, infections, malignancies or due to genetic factors and very rarely idiopathic. Our case exemplifies premature calcification of costal cartilages. The patient was a 20-year-old lady, referred to endocrine clinic in UMS polyclinic, Kingfisher, University Malaysia Sabah for evaluation of metabolic and endocrine causes of premature costochondral calcification. Physical examination findings were normal except mild tenderness over the left lower lateral part of the chest. Investigation results were inconclusive to detect any underlying endocrine, metabolic or inflammatory conditions. Chest X-Ray revealed bilateral calcification of the 10th, 11th and 12th costal cartilages and was diagnosed as idiopathic calcification of costal cartilage. Only analgesics were given as treatment and the pain subsided after few days.

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Das adrenogenitale Syndrom im Kindesalter

Cited by 21 publications

References 137 publications

Premature Calcifications of Costal Cartilages: A New Perspective

Premature Calcifications of Costal Cartilages: A New Perspective

Die Formierung von gender am “Naturexperiment” Intersexualität in der zweiten Hälfte des 20. Jahrhunderts

Premature idiopathic costochondral calcification: A Case Report

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