Craniomaxillofacial Fibrous Dysplasia: Conservative Treatment and Maxillary Osteotomy Using the Schuchardt-Kufner Technique

Galiè, Manlio; Carnevali, Giulia; Elia, Giovanni; Pedriali, Massimo; Clauser, Luigi

doi:10.1055/s-0036-1597584

Cited by 4 publications

(4 citation statements)

References 13 publications

(33 reference statements)

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“…La DF fue descrita por primera vez en 1891 por Von Recklinghausen (8). Lichtenstein y Jaffe, en 1938, utilizaron por primera vez el término de displasia fibrosa (9,10).…”

Section: Discussionunclassified

Displasia fibrosa monostótica craneofacial

Carías

Díaz

2022

Acta otorrinolaringol cir cabeza cuello

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La displasia fibrosa es una enfermedad benigna del hueso, de base genética y de progresión lenta, que se caracteriza por el reemplazo progresivo del hueso normal por tejido fibrótico. El proceso puede afectar un solo hueso o múltiples huesos (displasia fibrosa monostótica o poliostótica); esta última puede estar asociada con enfermedades sindrómicas, como el síndrome de McCune-Albright. Objetivo Revisar el diagnóstico y tratamiento de los pacientes con displasia fibrosa craneofacial. Materiales y métodos Se realizó una revisión de artículos científicos, en revistas indexadas en línea como técnica para la recolección de información relevante en bases de datos como Scielo, Google Académico, Scopus, PubMed, y Dynamed, con artículos publicados en inglés y español. El periodo de revisión tuvo como límite el 01 de junio de 2020. Los términos de búsqueda fueron: “displasia fibrosa”, “displasia fibrosa monostótica”, y “displasia fibrosa craneofacial”. Obteniéndose 33 artículos. Conclusión La displasia fibrosa monostótica craneofacial es una enfermedad rara, que afecta principalmente la mandíbula, el hueso maxilar y el cornete inferior. Puede cursar asintomática o presentar deformidades faciales, dolor y trastornos visuales. Su diagnóstico es principalmente por estudios de imágenes y la biopsia. El tratamiento quirúrgico debe de ser bien planeado en cada uno de los pacientes, enfocado a deformidades faciales, evitar los trastornos visuales y es necesario cuando se maligniza la lesión.

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“…La DF fue descrita por primera vez en 1891 por Von Recklinghausen (8). Lichtenstein y Jaffe, en 1938, utilizaron por primera vez el término de displasia fibrosa (9,10).…”

Section: Discussionunclassified

Displasia fibrosa monostótica craneofacial

Carías

Díaz

2022

Acta otorrinolaringol cir cabeza cuello

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“…Clinically, progressive swelling in affected area without pain was the most common chief complaint [3]. Other symptoms may include facial asymmetry, pathological fractures, and nerve compression [4,5]. With deformation of the ocular bones, the optic canal becomes fragile due to its location in the center area.…”

Section: Introductionmentioning

confidence: 99%

Visual Field Improvement Achieved by Decompression Surgery for Craniomaxillofacial Fibrous Dysplasia: A Case Report

Li¹,

Chen²,

Tian³

et al. 2020

Preprint

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BackgroundCraniomaxillofacial fibrous dysplasia (CFD) is a type of congenital benign bone disorder that progressively replaces the healthy bone marrow with fibrous tissue. When the optic nerve is influenced, the efficacy of therapeutic decompression is doubtful, as vision loss is irreversible with the thinning nerve fiber layer. Case presentationA 22-year-old female presented to our institution with left painless, slowly-progressing orbito-fronto-temporal swelling. She had undergone several plastic surgeries before. Enlargement in her left frontal area involving the orbital region was seen, with increased frontal contour and vertical dystopia and minimal inferior displacement of the globe. We observed significant visual field defects in her left eye, and her retinal fiber layer was thin on examination. She was therefore diagnosed as FD. Decompression operation was performed, and her visual acuity and central visual field improved in the 1-month follow-up.Conclusions Our case indicated that visual defect caused by prolonged time course of optic nerve compression by craniomaxillofacial fibrous dysplasia can be relieved partially by decompression surgery.

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“…2 Fibrous dysplasia may affect single or multiple bones. 3 The Polyostotic form of the disease has nearly 100% involvement of the craniofacial bones. 4 The diagnosis of fibrous dysplasia is based on the correlation between the clinical, radiological and histological aspect, which constitutes a challenge in clinical practice.…”

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confidence: 99%

“…5 Fibrous dysplasia is considered a rare bone disease that represents 2.5% of all bone diseases and 7% of all benign bone tumors. 3,6 In general, FD presents in three forms; monostotic, polyostotic, and polyostotic with endocrinopathies, which can be associated with hyperpigmentation and endocrinological disorders and is called McCune-Albright syndrome. 7 The most commun form is monostotic.…”

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confidence: 99%

Mandibular Fibrous Dysplasia in Cotton Wool Appearance: A Rare Case Report

Loubna¹,

Taleb²

2020

Int J Oral Health Med Res

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Fibrous dysplasia is pathology of bone development in which the normal bone is replaced by a disorganized fibrous bone. This condition is considered rare in the maxilla. Usually, its evolution is progressively along the years, leading to an asymmetry whose aesthetic prejudice may be important. Other manifestations are also found, such as pain, paraesthesia, or malocclusion. There are several radiological aspects of fibrous dysplasia. The most common form is the "ground glass" appearance. The appearance in "cotton wool" being less found. We present a rare case of fibrous dysplasia in a 50-year-old woman. The diagnosis was made after a complete clinical examination including examination of the patient, radiological examination, and incisional biopsy. The patient is regularly monitored in our department.

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Craniomaxillofacial Fibrous Dysplasia: Conservative Treatment and Maxillary Osteotomy Using the Schuchardt-Kufner Technique

Cited by 4 publications

References 13 publications

Displasia fibrosa monostótica craneofacial

Displasia fibrosa monostótica craneofacial

Visual Field Improvement Achieved by Decompression Surgery for Craniomaxillofacial Fibrous Dysplasia: A Case Report

Mandibular Fibrous Dysplasia in Cotton Wool Appearance: A Rare Case Report

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