“…Collagen type III glomerulopathy (Col3GP), also known as collagenofibrotic glomerulopathy, is a rare renal disease described in humans and several animal species. 1,2,4 –6,8–10,12 –17 Individuals with Col3GP accumulate abundant type III collagen and, to a lesser extent, fibronectin and type V collagen in the mesangium and subendothelial space, adjacent to the glomerular basement membrane. This differs from the normal glomerular extracellular matrix, which contains type IV collagen, fibronectin, and other components, but lacks type III collagen.…”