Congenital pancreatic cysts in children

Boulanger, Scott C.; Borowitz, Drucy; Fisher, John F.; Brisseau, Guy F.

doi:10.1016/s0022-3468(03)00197-0

Cited by 30 publications

(23 citation statements)

References 5 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…True pancreatic cysts possess a true epithelium and frequently present themselves as solitary, unilocular, nonenzymatic, sterile, fluid-filled cystic lesions originating generally from the pancreatic tail or body [2,3]. Congenital true pancreatic cyst may exist in isolation or in association with such systemic diseases as BeckwithWiedemann syndrome, polycystic disease of the pancreas and kidneys, and von Hippel-Lindau disease [2,5,6]. Embryologically, it is accepted that true cysts occur as a result of developmental anomalies related to the sequestra- tion of primitive pancreatic ducts [6].…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Congenital true pancreatic cyst detected prenatally in neonate: a case report

Chung

Lim

Song

2007

Journal of Pediatric Surgery

View full text Add to dashboard Cite

Section: Discussionmentioning

confidence: 99%

“…Clinically, it presents incidentally or with polyhydramnios. Postnatal presentations have included an asymptomatic abdominal mass, abdominal distension, vomiting owing to gastric mass effect, and jaundice owing to biliary obstruction [3][4][5][6].…”

Section: Discussionmentioning

confidence: 99%

Congenital true pancreatic cyst detected prenatally in neonate: a case report

Chung

Lim

Song

2007

Journal of Pediatric Surgery

View full text Add to dashboard Cite

“…Congenital pancreatic cysts are rare entities [1][2][3][4][5]. Most pancreatic cysts in children are acquired pseudocysts resulting from trauma or pancreatitis.…”

Section: Discussionmentioning

confidence: 99%

“…In a recent review, we documented 25 reported cases of solitary pancreatic cysts [5]. Fourteen of these were diagnosed in patients under the age of two, and two were diagnosed pre-natally by ultrasound.…”

Section: Discussionmentioning

confidence: 99%

Congenital pancreatic cyst arising from occlusion of the pancreatic duct

Boulanger

Gosche

2007

Pediatr Surg Int

View full text Add to dashboard Cite

Congenital pancreatic cysts, particularly solitary cysts, are rare causes of abdominal masses in newborns. The etiology of these cysts is unknown and they can vary in location within the pancreas. We present a novel case of an infant with a solitary congenital cyst of the pancreatic duct, itself, as a result of occlusion of the pancreatic duct. Solitary congenital pancreatic cysts are a rare cause of abdominal masses in infants. We recently evaluated a 7-week-old infant with progressive abdominal distension since birth. This child was found to have a large solitary pancreatic cyst. This cyst resulted from occlusion of the main pancreatic duct at the level of the ampulla resulting in cystic degeneration of the pancreatic duct. Based on our review of the literature we believe this is the first documented case of such a cyst.

show abstract

“…Other congenital syndromes: Cystic transformation of the pancreas has been described in a variety of congenital syndromes 235 including Ivemark, trisomy 13 or 15, Meckel-Gruber, Elejalde, glutaric aciduria, chondrodyplasia, short rib polydactyly (Jeune's and Saldino-Noonan), 236 a newly described syndrome (Balci 237 ) and others with no specific name. 238 A patient with choledochal cyst was also reported to have multiple pancreatic cysts.…”

Section: Congenital or Developmental Cystsmentioning

confidence: 99%

Cystic lesions of the pancreas

Adsay

2007

Modern Pathology

188

View full text Add to dashboard Cite

Although cystic tumors of the pancreas are relatively rare, they constitute an increasingly important category. Advances in imaging and interventional techniques and the sharp drop in the mortality rate of pancreatic surgery have rendered pancreatic biopsies and resections commonplace specimens. Consequently, in the past two decades, the nature of many cystic tumors in this organ has been better characterized. The names of some existing entities were revised; for example, what was known as papillary-cystic tumor is now regarded as solidpseudopapillary tumor. New entities, in particular, intraductal papillary mucinous neoplasm and its variants, such as oncocytic and intestinal subtypes were recognized. The importance of clinical and pathologic correlation in the evaluation of these lesions was appreciated, in particular, with regards to the multifocality of these lesions, their association with invasive carcinomas, and thus their 'preinvasive' nature. Consensus criteria for the distinction of these from the ordinary precursors of adenocarcinoma, the pancreatic intraepithelial neoplasia, were established. The definition of mucinous cystic neoplasms was refined; ovarian-like stroma has now become almost a requirement for the diagnosis of mucinous cystic neoplasia, and defined as such, the propensity of these tumors to occur in perimenopausal women became even more striking. The validity and clinical value of classifying the pancreatic cysts of mucinous type as adenoma, borderline, CIS and invasive have been established. Related to this, the importance of thorough sampling in accurate classification of these mucinous lesions was recognized. Greater accessibility of the pancreas afforded by improved invasive as well as noninvasive modalities has also increased the detection of otherwise clinically silent cystic tumors, which has led to the recognition of more innocuous entities such as acinar cell cystadenoma and squamoid cyst of pancreatic ducts. As the significance of the cystic lesions emerged, cystic forms of otherwise typically solid tumors were also better characterized. Thus, significant developments have taken place in the classification and our understanding of pancreatic cystic tumors in the past few years, and experience with these lesions is likely to grow exponentially in the coming years. Modern Pathology (2007) 20, S71-S93.

show abstract

Congenital pancreatic cysts in children

Cited by 30 publications

References 5 publications

Congenital true pancreatic cyst detected prenatally in neonate: a case report

Congenital true pancreatic cyst detected prenatally in neonate: a case report

Congenital pancreatic cyst arising from occlusion of the pancreatic duct

Cystic lesions of the pancreas

Contact Info

Product

Resources

About