Congenital intrascleral cyst

Abstract

Congenital intrascleral cysts are rare. They are mostly located at the limbus with corneal involvement. We report a case of a 30-month-old boy with a bulber conjunctival cyst noticed at birth. The lesion enlarged over the following months but did not involve the cornea. During surgery the cyst proved to be intrascleral and a complete excision was carried out. The remaining defect was repaired with banked fascia lata. The histopathology revealed a scleral cyst wall lined by nonkeratinizing squamous epithelium with no goblet cells. We conclude that congenital intrascleral epithelial cysts are rare but should be considered in differential diagnosis of external eye cystic lesions. In our case, early excision and repair with fascia lata led to an uncomplicated postoperative course of 6 years.

Primary Corneoscleral Cyst in a Pediatric Patient

“…Similar to our case, most of the reported cases showed the cyst wall to be lined with epithelial cells [ 1 , 3 , 4 , 5 ]. Cases of cysts being associated with ghost cells causing hematic cyst and presence of lacrimal tissue within the cyst have also been reported [ 4 , 6 ].…”

“…Corneoscleral cyst can occur primarily or secondary to trauma or surgery. In the early stage, it may present as intrascleral cyst without corneal component [ 1 , 2 , 3 ].…”

“…Covering the excised cyst with a lamellar corneal graft, amniotic membrane, the preserved sclera, or the fascia lata reduces the risk of staphyloma formation [ 1 , 6 ]. Lamellar keratoplasty after excision of a cyst has also been reported [ 10 ].…”