Congenital Ectropion Uveae with Glaucoma

Ritch, Robert; Forbes, Max; Hetherington, John; Harrison, Raymond; Podos, Steven M.

doi:10.1016/s0161-6420(84)34288-9

Cited by 83 publications

(86 citation statements)

References 13 publications

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“…There have been several excellent reports about this clinical entity and its association with glaucoma [3][4][5]. In our patient ectropion uveae was diagnosed at birth with no tendency of progression during the following 15 years of life, thus supporting the suggestion of a nontractive ectropion.…”

Section: Discussionsupporting

confidence: 80%

“…In contrast to acquired tractive uveal ectropion in neovascular glaucoma or iridocorneoendothelial syndrome, primary congenital ectropion uveae does not progress. Association with neurofibromatosis, facial hemihypertrophy and Prader-Willi syndrome is well documented [4]. An abnormal migration of neural crest cells is supposed to induce this anterior segment malformation with dysgenetic signs of the angle structures often reported.…”

Section: Introductionmentioning

confidence: 98%

“…An abnormal migration of neural crest cells is supposed to induce this anterior segment malformation with dysgenetic signs of the angle structures often reported. Severe unilateral glaucoma occurs with high frequency [4,5]. Dysgenetic alterations of the posterior ocular segment in association with congenital ectropion uveae have not been described as yet.…”

Section: Introductionmentioning

confidence: 99%

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Primary Congenital Ectropion uveae Associated with Vitreoretinal Degeneration

Dietlein¹,

Jacobi²

1997

Ophthalmologica

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Primary congenital ectropion uveae is an extremely rare ocular malformation frequently associated with unilateral glaucoma. We report on a 15-year-old boy with unilateral congenital ectropion uveae, glaucoma and transvitreal strands in an optically empty vitreous. Dark adaptation was normal, but scotopic ERG showed subnormal b-wave amplitudes in the affected eye, which is a typical finding in hereditary vitreoretinal degenerations. The coincidence of primary congenital ectropion uveae and unilateral vitreoretinal degeneration without a family history seems to be sporadic and very extraordinary but could be due to a common defect of maturation.

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Section: Discussionsupporting

confidence: 80%

Section: Introductionmentioning

confidence: 98%

Section: Introductionmentioning

confidence: 99%

See 1 more Smart Citation

Primary Congenital Ectropion uveae Associated with Vitreoretinal Degeneration

Dietlein¹,

Jacobi²

1997

Ophthalmologica

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“…[1][2][3][4][5][6][7] Not all cases have systemic associations, however. None of the nine patients reported by Dowling et al 3 had any systemic associations.…”

Section: Commentmentioning

confidence: 99%

Bilateral juvenile glaucoma with iridotrabecular dysgenesis, congenital ectropion uveae, and thickened corneal nerves

Sethi

Pal

Dada

2004

Eye

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“…Glaucoma is frequently found with CIE, but not always. An abnormal migration of neural crest cells is thought to induce this anterior segment malformation with dysgenetic signs of the angle structures [1,2]. Although the actual anomaly is nonprogressive, multiple studies have shown the progression of open-angle glaucoma due to angle dysgenesis [2][3][4][5][6].…”

Section: Introductionmentioning

confidence: 99%

Congenital iris ectropion associated with juvenile glaucoma

Seymenoğlu

Başer

2010

Int Ophthalmol

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Congenital iris ectropion is an uncommon malformation of the anterior segment of the eye. The authors describe a case of bilateral congenital iris ectropion associated with juvenile glaucoma in an otherwise healthy 9-year-old girl. Intra-ocular pressure (IOP) measured by Goldmann applanation tonometry was 40 mmHg in the right eye and 32 mmHg in the left eye. Despite maximum IOP lowering therapy, the desired IOP levels needed to prevent further progression of the glaucoma could not be achieved. Visual field testing and confocal scanning laser tomography showed glaucomatous neuropathy. Trabeculectomy with antimetabolites (mitomycin C 0.2 mg/ml) was performed in both eyes and IOP was normalized without IOP lowering medications during a follow-up of 4 years. The authors point out the importance of recognizing congenital iris ectropion early to prevent blindness in young patients and improve their prognosis.

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Congenital Ectropion Uveae with Glaucoma

Cited by 83 publications

References 13 publications

Primary Congenital Ectropion uveae Associated with Vitreoretinal Degeneration

Primary Congenital Ectropion uveae Associated with Vitreoretinal Degeneration

Bilateral juvenile glaucoma with iridotrabecular dysgenesis, congenital ectropion uveae, and thickened corneal nerves

Congenital iris ectropion associated with juvenile glaucoma

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