Congenital atresia of the left coronary artery - myocardial revascularization in two children

Gebauer, Roman; Černý, Štěpán; Vojtovič, Pavel; Tax, Petr

doi:10.1510/icvts.2008.184317

Cited by 26 publications

(17 citation statements)

References 4 publications

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“…Most patients with LMCAA are symptomatic and fail to thrive. Myocardial infarction during infancy and frequent syncopial episodes from tachyarrhythmias may lead to sudden death during childhood or adolescence [3].…”

Section: Discussionmentioning

confidence: 99%

Congenital mitral regurgitation due to papillary muscle infarction: a case report and approach to evaluation

Ahmad¹,

Haw

Vettukattil

2009

Eur J Pediatr

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Congenital mitral regurgitation is relatively rare. It can be due to congenital malformation of the valve apparatus, associated structural heart defects, or results from myocardial dysfunction leading to deformation of the valve annulus. Hence, careful delineation of the pathologic processes involved in the mechanism is critical when evaluating patients presenting with congenital mitral valve regurgitation. Congenital anomalies of the coronary system are one of the serious associations, which needs prompt recognition and treatment to prevent fatal complications. We report a case of congenital atresia of left main coronary artery in an asymptomatic 8-month-old presenting with an incidental finding of mitral valvar regurgitation. Appropriate investigations and management lead to restoration of normal coronary blood flow and valve function. This particular case illustrates that congenital coronary anomalies may present in an otherwise asymptomatic child. It should be considered as one of the possible differential diagnosis in unexplained mitral regurgitation. Early recognition and prompt surgical treatment can radically modify the prognosis.

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Section: Discussionmentioning

confidence: 99%

Congenital mitral regurgitation due to papillary muscle infarction: a case report and approach to evaluation

Ahmad¹,

Haw

Vettukattil

2009

Eur J Pediatr

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“…The LMCA ostial atresia is seen more commonly than the RCA ostial atresia. In case of coronary ostial atresia, the proximal portion ends blindly and blood comes from the other main coronary artery via small collateral pathways such as Vieussens' arterial ring and the Kugel anastomotic artery (38). This coronary anomaly is hemodynamically significant and almost all patients are symptomatic.…”

Section: Anomalies Of Intrinsic Coronary Arterial Anatomy Congenital mentioning

confidence: 99%

“…They usually present with failure to thrive and myocardial infarction in infancy, and syncope in children and adolescents (39). Small caliber collateral circulation is not adequate to the heart and almost all patients need surgical revascularization to prevent the development of myocardial ischemia (38,39).…”

Section: Anomalies Of Intrinsic Coronary Arterial Anatomy Congenital mentioning

confidence: 99%

Evaluation of anatomy, variation and anomaly of the coronary arteries with coronary computed tomography angiography

Erol¹,

Koplay²,

Paksoy³

2012

Anadolu Kardiyol Derg

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Recent technical advances in computed tomography (CT) have improved image quality, diagnostic performance and accuracy of coronary CT angiography (CCTA). Latest dose-reduction strategies reduce radiation dose to an acceptable level even lower than that from conventional coronary angiography. CCTA is a noninvasive imaging modality which can effectively show complex coronary artery anatomy, variations and congenital anomalies of the coronary arteries. Congenital coronary artery anomalies are rare entities, but sometimes have a potential of producing fatal consequences. CCTA is now the primary imaging modality for the evaluation and diagnosis of coronary artery anomalies. Reporters should, therefore, have knowledge of the normal coronary artery anatomy and variations, and understand the different types of coronary artery anomalies and their respective prognostic implications in order to provide correct diagnosis and to prevent undesirable mistakes during interventional and surgical procedures. (Anadolu Kardiyol Derg 2013; 13: 154-64) Key words: Coronary artery anatomy, variation, anomalies, coronary computed tomography angiography Review Derleme 154ÖZET Bilgisayarlı tomografi (BT) teknolojisinde yaşanan teknik ilerlemeler koroner BT anjiyografinin görüntü kalitesinde, tanısal performansında ve doğ-ruluğunda iyileşmelere yol açmıştır. Yeni geliştirilen doz düşürmeye yönelik stratejiler sayesinde radyasyon dozu kabul edilebilir düzeylere ve hatta konvansiyonel koroner anjiyografi değerlerinin altına inmiştir. Koroner BT anjiyografi invaziv olmayan bir görüntüleme yöntemi olup koroner arterlerin kompleks anatomisini, varyasyonlarını ve konjenital anomalilerini etkili bir şekilde göstermektedir. Konjenital koroner arter anomalileri nadir görülen patolojiler olsa da bazen hayatı tehdit edebilen sonuçlar doğurma potansiyeline sahiptir. Koroner BT anjiyografi günümüzde koroner arter anomalilerinin tanısında primer görüntüleme yöntemi olarak kullanılmaktadır. Bu nedenle raporlayıcıların doğru tanı koyabilmeleri ve cerrahi ve girişimsel işlemler sırasında istenmeyen hataları önleyebilmeleri için koroner arter anatomisini, varyasyonlarını ve koroner arter anomalilerinin farklı tiplerini ve bunların prognostik sonuçlarını bilmeleri gereklidir. (Anadolu Kardiyol Derg 2013; 13: 154-64) Anahtar kelimeler: Koroner arter anatomisi, varyasyon, anomali, koroner bilgisayarlı tomografi anjiyografi

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“…Congenital anomaly of the coronary arteries is a rare disease occurring in 1%-2% of all congenital heart diseases. Atresia of the left main coronary artery is one of its least-frequently observed variations, with very few cases presented in the literature (Amaral et al, 2000;Gebauer et al, 2008). The prognosis is unfavorable because it results in myocardial ischemia or infarction, and even sudden cardiac death.…”

Section: Introductionmentioning

confidence: 99%

Congenital atresia of the left main coronary artery in an infant

Sohn

Jang

Choi

2010

J. Zhejiang Univ. Sci. B

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Congenital atresia of the left main coronary artery is a rare occurrence, and surgical revascularization-bypass graft is required. We here report a rare case of congenital coronary anomaly in an infant. A 10-month-old male infant was admitted to the hospital with heart failure symptoms. Echocardiographic examinations revealed mitral valve regurgitation and ischemic changes of the anterolateral papillary muscle and chordae. Coronary angiography showed atresia of the left main coronary artery with a severe hypoplastic left anterior descending artery and a circumflex coronary artery. Unfortunately, sudden cardiac arrest occurred after catheterization and the infant did not recover despite of immediate cardiopulmonary resuscitation. Further studies are needed to find a newer diagnostic method to detect coronary anomaly in an infant, and coronary angiography, if necessary, has to be performed very carefully.

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Congenital atresia of the left coronary artery - myocardial revascularization in two children

Cited by 26 publications

References 4 publications

Congenital mitral regurgitation due to papillary muscle infarction: a case report and approach to evaluation

Congenital mitral regurgitation due to papillary muscle infarction: a case report and approach to evaluation

Evaluation of anatomy, variation and anomaly of the coronary arteries with coronary computed tomography angiography

Congenital atresia of the left main coronary artery in an infant

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