Computed tomography findings in bilateral perinephric lymphangiomatosis

Abstract

Perinephric lymphangioma is rare disorder that may be confused with various forms of renal cystic diseases and urinomas. In this disorder a developmental malformation results in failure of developing lymphatic tissue to establish normal communication with the rest of lymphatic system. Once there is restricted drainage of lymphatic fluid the lymphatic channels dilate to form cystic masses that may be unilocular or multilocular and may be seen unilaterally or bilaterally .This condition presents with various signs and symptoms or can be just an incidental finding which in presence of misleading clinical history may be confused with other diseases. CT scan with delayed cuts and USG guided aspiration with biochemical analysis of fluid will help us in arriving to final diagnosis.

Linfangiectasia renal unilateral: Caso clínico

“…Intentar resecarlos es muy dificultoso y habitualmente se producen lesiones que obligan a una nefrectomía 11,12 . También se ha comunicado la injección de sustancias esclerosantes como alcohol y bleomicina 2 . Las biopsias renales o de los riñones obtenidos en las nefrectomías muestran gloméru-los y túbulos normales, en el intersticio en cambio, hay espacios tapizados por una delgada capa de células endoteliales en el parénquima, que con inmunohistoquímica su positividad para el factor VIII permiten diferenciarlo de un recubrimiento epitelial.…”

“…Sus localizaciones más frecuentes son el cuello (70%) y la axila (20%) 1 . La linfangiectasia renal (LFR) es de muy baja frecuencia y puede confundirse con otras patologías quísticas del riñón 2 . La LFR ha sido descrita con diversos nombres como: linfangioma renal, linfangiectasia peri-pélvica, enfermedad poliquística del seno renal, higroma renal y linfangiectasia renal peripélvica multiquística.…”

Sonography of perinephric fluid collections: A pictorial essay

“…Renal lymphangiomatosis is a benign disease involving renal lymphatics. It is also known as renal lymphangioma, renal lymphangiectasia, peripelvic lymphangiectasia, or renal peripelvic multicystic lymphangiectasia . This disorder is characterized by ectasia of the peripelvic (intrarenal) or perirenal (extrarenal) lymphatic vessels with abnormal distension of the lymphatic ducts due to a failure of communication with the larger retroperitoneal lymphatic vessels.…”

“…A large amount of this lymphatic fluid may be confused with ascites . US‐guided aspiration followed by biochemical analysis of the collected fluid may assist in the correct diagnosis …”

Bilateral Renal Lymphangiectasia: Radiological Findings by Ultrasound, Computed Tomography, and Magnetic Resonance Imaging

“…[ 1 ] Lymphangiectasia is a developmental disorder with failure of development of normal communication between the lymphatic tissue and the rest of the lymphatic system leading to lack of normal drainage of lymphatic fluid with subsequent cystic dilatation of the lymphatic channels. [ 2 ]…”