Common atrium: A rare congenital heart anomaly

Demirelli, Selami

doi:10.5543/tkda.2015.93027

Cited by 3 publications

(5 citation statements)

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“…They can present with dyspnea on exertion, hypoxia, cyanosis, and developmental delay. Patients mostly are diagnosed during early years; however, few case reports described patients progressing to young adulthood before being diagnosed with CA [5–10]. Echocardiography is usually the first step in diagnosing CA [10].…”

Section: Discussionmentioning

confidence: 99%

“…Patients mostly are diagnosed during early years; however, few case reports described patients progressing to young adulthood before being diagnosed with CA [5–10]. Echocardiography is usually the first step in diagnosing CA [10]. IA and further investigative methods do help in the evaluation of coexistent congenital abnormalities.…”

Section: Discussionmentioning

confidence: 99%

“…The primary objective of surgery is to reconstruct the atrial septum and correct associated congenital abnormalities. Early diagnosis is crucial as the development of Eisenmenger syndrome is a contraindication to surgery [10, 22].…”

Section: Discussionmentioning

confidence: 99%

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A Unique and Rare Presentation of Adult Congenital Heart Disease: Common Atrium Associated with Coronary Aneurysms and Fistula

Rawala

Muñoz

Pervaiz

2019

Case Reports in Cardiology

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An atrial septal defect is the second most common congenital heart disease found in adults with a female to male ratio of 4 : 1. However, it is rare to have a complete absence of the interatrial septum (IAS) to be diagnosed in an elderly patient associated with other coexisting anomalies. We present a case of a 60-year-old female presenting with common atrium, coronary arteriovenous fistula, and coronary artery aneurysms. This case highlights rare adult congenital cardiac anomalies and the importance of thorough workup to evaluate for the intracardiac shunt in a patient who has right heart enlargement and development of pulmonary disease in adulthood without a significant history of chronic smoking. A 60-year-old female patient presented with substernal chest pain. The nuclear stress test showed no reversible ischemia; however, right ventricle (RV) dilation was present. The patient underwent further evaluation for RV dilation with a transthoracic echocardiogram that demonstrated a complete absence of IAS and was confirmed by a positive bubble study. The patient had an invasive angiography that showed severely elevated RV pressure. Oxygen saturation in the right atrium was higher than in the inferior vena cava. Hence, an intracardiac shunt with a 10% increase in oxygen saturation was identified. It also identified aneurysmal coronary arteries (measuring 0.8 to 1.0 cm). Cardiac computed tomography angiogram was performed that identified all coronary arteries to be ectatic/aneurysmal measuring up to 8-10 mm, an absence of IAS, and a possible fistula between the distal left anterior descending and a coronary vein. To our knowledge, this is the first-ever presentation of a complete congenital absence of IAS in a patient who has survived into adulthood with the development of severe pulmonary hypertension without Eisenmenger syndrome. It is unclear at this point if surgical treatment to correct the anatomical defect (which would be probably palliative) would be superior to conservative medical therapy. Besides, the presence of coronary arteriovenous fistula would make the decision-making process more complex regarding surgical versus conservative management.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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A Unique and Rare Presentation of Adult Congenital Heart Disease: Common Atrium Associated with Coronary Aneurysms and Fistula

Rawala

Muñoz

Pervaiz

2019

Case Reports in Cardiology

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“…Asuman Kaftan et al 8) reported a similar case of undiscovered common atrium in a 23-year-old patient. In addition, Demirelli et al 9) reported a case of incidentally diagnosed asymptomatic common atrium in a 23-year-old woman, while Hasanin and Kinsara 10) reported a case of late-discovered common atrium in a patient with persistent left superior vena cava. However, to our knowledge, our case is the oldest patient with common atrium to have remained asymptomatic.…”

Section: Discussionmentioning

confidence: 99%

Well-Tolerated and Undiscovered Common Atrium until Late Adulthood

Kim

Choi

Doo

et al. 2016

J Cardiovasc Ultrasound

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“…Echocardiography is usually the first step in diagnosing single atrium and is extremely helpful and beneficial, in the evaluation of coexistent congenital abnormalities [11].…”

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confidence: 99%

Situs ambiguous with three chambered heart (single atrium), evaluation by four-dimensional X-strain color echocardiography – A case report

Mehrotra¹,

Sharma²,

Singh³

et al. 2022

Indian J Child Health

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Situs ambiguous accounts for 4% of all congenital heart disease (CHD) and has an incidence of 1:10,000 new born births. To standardize the nomenclature for CHD, the international nomenclature society published a globally accepted nomenclature tree for CHD with the 11th Iteration of international classification of disease. According to this publication common atrium, single atrium and atrium communis are denoted as synonyms. The incidence of common atrium among atrial septal defect (ASD) patients is 3–4% only and thus denoting it to be a rare entity. We are presenting an exceedingly rare case of a patient of situs ambiguous, left isomerism, and single atrium with a cleft on the anterior mitral leaflet, evaluated comprehensively by four-dimensional X-strain color Doppler echocardiography.

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Common atrium: A rare congenital heart anomaly

Cited by 3 publications

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A Unique and Rare Presentation of Adult Congenital Heart Disease: Common Atrium Associated with Coronary Aneurysms and Fistula

A Unique and Rare Presentation of Adult Congenital Heart Disease: Common Atrium Associated with Coronary Aneurysms and Fistula

Well-Tolerated and Undiscovered Common Atrium until Late Adulthood

Situs ambiguous with three chambered heart (single atrium), evaluation by four-dimensional X-strain color echocardiography – A case report

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