Well-Tolerated and Undiscovered Common Atrium until Late Adulthood

Kim, Kyungjoong; Choi, Jiwook; Doo, Youngjae; Yun, Yeong Seop; Kim, Jong-Wook; Lee, Beom Jae

doi:10.4250/jcu.2016.24.3.243

Cited by 5 publications

(7 citation statements)

References 9 publications

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“…Bun et al 3 documented a 57-year-old woman, who presented with common atrium and mitral valve cleft. Likewise, Kim et al 7 diagnosed common atrium with atrioventricular defect in a 48-year-old man. Altıntaş et al 4 described a 43-year-old woman, who had SA without mitral valve cleft.…”

Section: Discussionmentioning

confidence: 93%

A 78-year-old man diagnosed with single atrium as congenital heart disease

Azaje,

Abebe,

Fentahun

et al. 2023

SAGE Open Medical Case Reports

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Single atrium is a rare congenital heart disease characterized by complete absence of the interatrial septum. It occurs as an isolated cardiac defect, or as a part of skeletal, muscular, ophthalmologic, and vascular malformations to signify congenital syndromes. A 78-year-old male patient presented with generalized body swelling of 2 weeks duration. He had associated shortness of breath, orthopnea, productive cough, and palpitation. Upon physical examination, blood pressure = 150/75 mmHg, pulse rate = 50 bpm, respiratory rate = 24 bpm, and T° = 36.7 °C. He had signs of pleural effusion on left lung field. Cardiovascular examination revealed mean heart rate of 50 beats/min with irregularly irregular pulse rhythm, raised jugular venous pressure, and pansystolic murmur at left lower sternal border. He had tender hepatomegaly, ascites, and pitting leg edema. Chest X-ray showed cardiomegaly, prominent pulmonary trunks, and left-sided pleural effusion. Electrocardiography revealed atrial fibrillation, bifascicular block (right bundle branch block and left anterior fascicular block) with mean heart rate of 50 beats/min. Two-dimensional transthoracic echocardiography showed complete absence of interatrial septum (single atrium) without atrioventricular defect and interventricular communication. Diagnosis of heart failure secondary to congenital heart disease (single atrium) with atrial fibrillation and bifascicular block was made based on clinical and imaging evaluation. Well-tolerated symptoms of a single atrium until late adulthood could be explained by the presence of streaming or incomplete mixing of blood within the atrium, in which the more oxygenated blood is directed to the systemic circuit.

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Section: Discussionmentioning

confidence: 93%

A 78-year-old man diagnosed with single atrium as congenital heart disease

Azaje,

Abebe,

Fentahun

et al. 2023

SAGE Open Medical Case Reports

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“…Single atrium is usually diagnosed in childhood, though adult presentation of the disease has also been reported. Patients present with decrease in exercise tolerance, shortness of breath, cyanosis, upper respiratory tract infections, fatigue, developmental delay, and heart failure [20]. Single atrium may be associated with different ventricular morphologies: Two ventricles, single right ventricle, single left ventricle, or an undifferentiated single ventricle.…”

Section: Discussionmentioning

confidence: 99%

“…TEE and TTE play a pivotal role in defining the anatomy of the single atrium and ruling out the classical partial AV septal defect; however, it lacks delineation of the extracardiac structures [14,15]. Patients with single atrium without any associated malformations usually have a good prognosis even without surgical management [20]. However, patients with associated malformations usually require surgical intervention [24].…”

Section: Discussionmentioning

confidence: 99%

Situs ambiguous with three chambered heart (single atrium), evaluation by four-dimensional X-strain color echocardiography – A case report

Mehrotra¹,

Sharma²,

Singh³

et al. 2022

Indian J Child Health

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Situs ambiguous accounts for 4% of all congenital heart disease (CHD) and has an incidence of 1:10,000 new born births. To standardize the nomenclature for CHD, the international nomenclature society published a globally accepted nomenclature tree for CHD with the 11th Iteration of international classification of disease. According to this publication common atrium, single atrium and atrium communis are denoted as synonyms. The incidence of common atrium among atrial septal defect (ASD) patients is 3–4% only and thus denoting it to be a rare entity. We are presenting an exceedingly rare case of a patient of situs ambiguous, left isomerism, and single atrium with a cleft on the anterior mitral leaflet, evaluated comprehensively by four-dimensional X-strain color Doppler echocardiography.

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“…CA patients without multiple malformations usually have a relatively long life expectancy, even without surgical intervention. [21,22] However, those with associated malformations who do not receive surgical treatment usually have a poor prognosis. [2–4] Delayed identification of CA increases the possibility of pulmonary vascular disease, progression to arrhythmia, even cardiac dysfunction.…”

Section: Discussionmentioning

confidence: 99%

“…[2–4] Delayed identification of CA increases the possibility of pulmonary vascular disease, progression to arrhythmia, even cardiac dysfunction. [21] Thus, the prompt diagnosis of CA, of the different ventricular types, and of the associated malformations contributes to the clinical treatments.…”

Section: Discussionmentioning

confidence: 99%

Common atrium and the associated malformations

Zhang¹,

Yang²,

Yang³

et al. 2018

Medicine

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Common atrium (CA) is a rare complex congenital heart disease. The studies of CA are mostly case reports, while few have been done regarding its morphological characteristics. We aimed to determine CA characteristics and diagnostic accuracy in assessing associated malformations in these patients with low-dose dual-source computed tomography (DSCT).Twenty-one pediatric and adolescent CA patients underwent low-dose DSCT. Different ventricular types and associated malformations were assessed. The diagnostic accuracy of DSCT and transthoracic echocardiography (TTE) in evaluating associated malformations were assessed. The effective doses of DSCT were calculated.Patients (n = 21) were divided into CA with biventricular physiology (n = 7) and CA with single ventricle (SV) (n = 14). There were 3 types of SV morphology: single left ventricle (n = 5), single right ventricle (n = 6), and undifferentiated ventricle (n = 3). In all, 22 associated malformations were seen in CA and 56 in CA with SV. DSCT was superior to TTE for detecting intracardiac anomalies (sensitivity: DSCT, 92.31% vs TTE, 76.92%), great vessels anomalies (sensitivity: DSCT, 100.00% vs TTE, 77.50%), and of collateral vessels (sensitivity: DSCT, 100% vs TTE, 20.00%). The estimated mean effective dose was 0.95 ± 0.44 mSv (<1 mSv).This study indicated that low-dose DSCT is an ideal alternative for pediatric and adolescent patients with CA, providing morphological details of CA and associated malformations with high accuracy.

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Well-Tolerated and Undiscovered Common Atrium until Late Adulthood

Cited by 5 publications

References 9 publications

A 78-year-old man diagnosed with single atrium as congenital heart disease

A 78-year-old man diagnosed with single atrium as congenital heart disease

Situs ambiguous with three chambered heart (single atrium), evaluation by four-dimensional X-strain color echocardiography – A case report

Common atrium and the associated malformations

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