Clinical profile of restrictive cardiomyopathy.

Benotti, Joseph R.; Grossman, William; Cohn, Peter F.

doi:10.1161/01.cir.61.6.1206

Cited by 160 publications

(68 citation statements)

References 5 publications

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“…14 A recent report describes eight cases from Saudi Arabia. 15 Our three cases satisfied both clinical and echocardiographic criteria for this diagnosis as suggested by Benotti et al 16 …”

Section: Restrictive Cardiomyopathysupporting

confidence: 74%

Cardiomyopathy in Saudi Arabia: The King Khalid University Hospital Experience

et al. 1988

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This is a study of the prevalence and clinical presentation of 112 cases of cardiomyopathy seen at a large teaching hospital in Riyadh. All patients satisfied the diagnostic criteria for cardiomyopathy defined by the World Health Organization/International Society and Federation of Cardiology (WHO/ISFC) in 1980. There were 101 patients with dilated cardiomyopathy, eight with hypertrophic cardiomyopathy, and three with restrictive cardiomyopathy. The clinical aspects of these patients form the subject of this study.

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“…14 A recent report describes eight cases from Saudi Arabia. 15 Our three cases satisfied both clinical and echocardiographic criteria for this diagnosis as suggested by Benotti et al 16 …”

Section: Restrictive Cardiomyopathysupporting

confidence: 74%

Cardiomyopathy in Saudi Arabia: The King Khalid University Hospital Experience

et al. 1988

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“…We believe that the observed clear reduction in both VE-MVG and RVF-MVG in the RCM group results from fibrotic and/or infiltrative processes involving the subendocardium and/or myocardium. 33,34 This process of structural and functional myocardial changes is typical for RCM rather than CP.…”

Section: Resultsmentioning

confidence: 99%

“…32 Conversely, in RCM, the LV wall is resistant to stretch due to myocardial or endocardial disease. 33 In this study, Doppler MVG was used to quantify structural/functional myocardial status by following the hypothesis that DMI has the potential to quantify changes in the intrinsic mechanical elastic properties of the myocardium. 19 Garcia et al 14 conducted the first pulsed-wave DMI study to measure mitral annulus longitudinal velocities to differentiate RCM from CP.…”

Section: Discussionmentioning

confidence: 99%

Differentiation Between Restrictive Cardiomyopathy and Constrictive Pericarditis by Early Diastolic Doppler Myocardial Velocity Gradient at the Posterior Wall

et al. 2000

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Background-The differential diagnosis between restrictive cardiomyopathy (RCM) and constrictive pericarditis (CP) is challenging and, despite combined information from different diagnostic tests, surgical exploration is often necessary. Methods and Results-A group of 55 subjects (mean age, 63Ϯ11 years; 36 men and 19 women) were enrolled in the study; 15 had RCM, 10 had CP, and 30 were age-matched, normal controls. The diagnosis of RCM was supported by a biopsy; in the CP group, the diagnosis was confirmed either surgically or at autopsy. All patients underwent a transthoracic echocardiogram that included the assessment of Doppler myocardial velocity gradient (MVG), as measured from the left ventricular posterior wall during the predetermined phases of the cardiac cycle. MVG was lower (PϽ0.01) in RCM patients compared with both CP patients and normal controls during ventricular ejection (2.8Ϯ1.2 versus 4.4Ϯ1.0 and 4.7Ϯ0.8 s Ϫ1 , respectively) and rapid ventricular filling (1.9Ϯ0.8 versus 8.7Ϯ1.7 and 3.7Ϯ1.4 s Ϫ1 , respectively). Additionally, during isovolumic relaxation, MVG was positive in RCM patients and negative in both CP patients and normal controls (0.7Ϯ0.4 versus Ϫ1.0Ϯ0.6 and Ϫ0.4Ϯ0.3 s Ϫ1 , respectively; PϽ0.01). During atrial contraction, MVG was similarly low (PϽ0.01) in both RCM and CP patients compared with normal controls (1.6Ϯ1.7 and 1.7Ϯ1.8 versus 3.8Ϯ0.9 s Ϫ1 , respectively). Conclusions-Doppler

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“…The "square root sign," characterized by a rapid dip and early plateau in the diastolic ventricular pressure, can be detected in both ventricles in 43% of patients, and end-diastolic equalization of pressure is found in 42%. 4,31 Restrictive cardiomyopathy can be differentiated from constrictive pericarditis, which presents with a similar clinical picture, by cardiac catheterization, radionuclide angiography, computed tomography, cardiac magnetic resonance imaging, and echocardiography by application of conventional Doppler and tissue-Doppler imaging. [32][33][34] If the Doppler tracings of the transmitral flow (Fig.…”

Section: Diagnosis By Echocardiography and Cardiac Catheterizationmentioning

confidence: 99%

“…4 A further study of nine patients reported only one death during a mean follow-up time of 22 months. 31 …”

Section: Prognosismentioning

confidence: 99%

Extracardiac Medical and Neuromuscular Implications in Restrictive Cardiomyopathy

Stöllberger

Finsterer

2007

Clinical Cardiology

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Restrictive cardiomyopathy (RCMP) is characterized by restrictive filling and reduced diastolic volume of either or both ventricles with normal or near‐normal systolic function and wall thickness. It may occur idiopathically or as a cardiac manifestation of systemic diseases such as scleroderma, amyloidosis, Churg‐Strauss syndrome, cystinosis, sarcoidosis, lymphoma, Gaucher's disease, hemochromatosis, Fabry's disease, pseudoxanthoma elasticum, hypereosinophilic syndrome, carcinoid, Noonan's syndrome, reactive arthritis, or Werner's syndrome and various neuromuscular disorders. Whereas in idiopathic RCMP the therapeutic options are only treatment of cardiac congestion, in cases with an underlying disorder, a causal therapy may be available. Patients with RCMP should be investigated as soon as the cardiac diagnosis is established for extracardiac diseases to detect a possibly treatable cause of RCMP before the disease becomes intractable. These investigations include a diligent clinical history and examination, blood tests, and ophthalmologic, otologic, dermatologic, gastroenterologic, nephrologic, hematologic, and neurologic examinations. If extracardiac examinations do not reveal a plausible cause for RCMP, endomyocardial biopsy is indicated. Copyright © 2007 Royal Meteorological Society

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Clinical profile of restrictive cardiomyopathy.

Cited by 160 publications

References 5 publications

Cardiomyopathy in Saudi Arabia: The King Khalid University Hospital Experience

Cardiomyopathy in Saudi Arabia: The King Khalid University Hospital Experience

Differentiation Between Restrictive Cardiomyopathy and Constrictive Pericarditis by Early Diastolic Doppler Myocardial Velocity Gradient at the Posterior Wall

Extracardiac Medical and Neuromuscular Implications in Restrictive Cardiomyopathy

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