Cavernous Lymphangioma Arising in the Chest Wall 19 Years after Excision of a Cystic Hygroma

Abstract

Lymphangioma is a congenital malformation of the lymphatic system and is thought to result from the failure of the lymphatic system to connect with the venous system. Lymphangioma of the chest wall is a very rare disease entity, and only a few cases have ever been documented in the literature. To the best of our knowledge, there have been few cases of recurrent cavernous lymphangioma after surgical excision of a cystic hygroma on the same side of the chest wall. Here, we report a case of a cavernous lymphangioma of the chest wall in a patient who had undergone surgical excision of a cystic hygroma 19 years earlier.

Giant Splenic Lymphangiomatosis in Adult: a Diagnostic Dilemma

“…More often, they consist of multiple cysts of varying sizes lined by flat endothelial cells, which contain eosinophilic serous fluid. The septa are made of fibrous connective tissue with rare vessels [5]. Splenic lymphangiomas are mostly asymptomatic; therefore, the final diagnosis should be based on a combination of clinical, radiological, and histopathological findings.…”

Simultaneous hemopericardium, hemoperitoneum and hemothorax after complete surgical resection of mediastinal cystic lymphangioma: A case report

“…Various alternative treatments for lymphangioma have been attempted; they include laser therapy, radiation therapy, chemotherapy and the use of sclerotizing agents [2,19]. The efficacy of these treatments is highly variable in incidental reports.…”

“…On CT scan and/or MRI scan, a cystic lymphangioma can be suggested based on multiseptated and loculated mass [12]. The gold standard treatment of lymphangioma is complete surgical resection [1,2,13]. However, due to the infiltrative nature of lymphangiomas, this procedure becomes incomplete and hard to use and can only be applied in 10-50% of the cases.…”

“…Therefore, recurrence represents an important problem, with a prevalence rate between 0% and 27% after total exeresis and between 15% and 53% after partial exeresis. [2,13,14].…”

“…It is most frequently observed in the head and neck, but can occur at any location in the body [1][2][3]. The exact incidence is unknown, but its prevalence is estimated to be between 0.01% and 4.5% of all mediastinal tumors [4][5][6].…”