“…So far, seven cases of atrophic pigmented dermatofibrosarcoma protuberans in addition to ours have been reported in PubMed, all presenting with a depressed pigmented plaque, three of which developed a nodule within the plaque [Table 1]. 4,[7][8][9][10] Due to their atypical presentations, various incorrect diagnoses were considered, including lipoatrophy, hemangioma and neurofibroma. 4,9 In our case, misdiagnosis of hyperpigmentation was made at initial visiting and only observation was recommended.…”