Cardiac Tumor in Juvenile Onset Behçet’s Disease: Case Report and Review of the Literature

Adams, Elizabeth E.; Aluquin, Vincent; Bingham, Catherine April; Stone, James R.; Pauliks, Linda B.

doi:10.1007/s00246-009-9565-4

Cited by 7 publications

(4 citation statements)

References 9 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…The frequency of recurrent eye involvement in JABD ranges from 7.5 to 80% [9,12,13,15,16,17,21,25,26,27,28,29,30,33,35]. In a recent cohort of 3,382 ABD patients, only 3.3% were younger than 15 years, whereas 31% of the children had been diagnosed with ocular involvement [15].…”

Section: Clinical Features Of Jabdmentioning

confidence: 99%

See 1 more Smart Citation

Juvenile Adamantiades-Behçet Disease

Vaiopoulos

Kanakis²,

Kapsimali

et al. 2016

Dermatology

View full text Add to dashboard Cite

Adamantiades-Behçet disease (ABD) is a chronic, multisystemic, recurrent, inflammatory vascular disorder of unknown etiology. Patients with symptoms initially appearing at the age of 16 or less are considered as cases of juvenile-onset ABD (JABD). JABD is relatively rare compared to ABD of adults, and only case reports and case studies have been published regarding this subtype of the disease. Epidemiology, clinical features, diagnosis and treatment of JABD are discussed in this review.

show abstract

Section: Clinical Features Of Jabdmentioning

confidence: 99%

“…Since the publication of the first article on the pediatric disease by Mundy and Miller in 1978 [8], several case reports and case studies have been described [6,7,9,10,11,12,13,14]. However, reviews on this subject are rather scarce [6,15,16,17,18].…”

Section: Introductionmentioning

confidence: 99%

Juvenile Adamantiades-Behçet Disease

Vaiopoulos

Kanakis²,

Kapsimali

et al. 2016

Dermatology

View full text Add to dashboard Cite

show abstract

“…To learn more about the cardiac involvement of pediatric BD, we used the search string "Behçet's, cardiac, pediatric" in PubMed (published between January 1990 and March 2021). There were 13 closely related publications, [10][11][12][13][14][15][16][17][18][19][20][21][22] and 14 cases of cardiac involvement in pediatric BD were summarized. There were no large-scale case studies on pediatric BD cardiac valvular involvement.…”

Section: Discussionmentioning

confidence: 99%

Pediatric Behçet's disease with cardiac valvular lesions: A case-based review

2023

View full text Add to dashboard Cite

Due to the insidious nature of pediatric cardiac Behçet's disease (BD), misdiagnosis or missed diagnosis occurred frequently. We described a female pediatric patient with BD with cardiac valvular involvement diagnosed at the age of 4 years with clinical symptoms, including aphthous ulcers, fever, perianal ulcers, and erythema nodosum, as well as significantly elevated inflammatory markers. Echocardiography revealed that previously absent aortic valve lesions developed later and gradually worsened. After being diagnosed with BD with cardiovascular involvement, the patient was treated with glucocorticoids, immunosuppressants, biologics, diuretics, and aortic valvuloplasty. At the time of the follow up, the patient was stable. A review of 13 publications was conducted, including 14 cases of cardiac involvement in pediatric BD.

show abstract

“…Azathioprine, colchicine and infliximab were the other used drugs. [5][6][7][20][21][22][23][24][25] Despite all combined treatment options, we could not avoid mortality in our case.…”

Section: Discussionmentioning

confidence: 99%

Is Immunosuppressive and Thrombolytic Therapy Really Effective in a Patient With Intracardiac Thrombosis and Pulmonary Artery Aneurysm due to Behçet’s Disease?

2019

View full text Add to dashboard Cite

Behçet's disease (BD) is a rare, multisystemic, chronic vasculitic disorder with unknown etiology. The most common signs of BD are recurrent aphthous oral ulcers, genital ulcers, ocular lesions, dermatological lesions, and arthritis. 1,2 BD may also affect the pulmonary and cardiovascular systems. 2-4 Frequency of BD is low but intracardiac thrombus (IcT) formation is even less common; this serious complication has been reported only as case reports. 5-7 Pulmonary artery aneurysm (PAA) is also very rare, and only a few pediatric patients have been reported in the literature. 6,7 IcT accompanying PAA is extremely rare in the pediatric age group. In this article, we present an unusual case of an adolescent patient with PAA and IcT who did not survive despite all medical therapies. CASE REPORT A 16-year-old male patient was admitted to the hospital with complaints of productive cough, fever, and chills. Despite oral amoxicillin/ clavulanic acid treatment, the patient's complaints increased; he developed shortness of breath and was admitted to another hospital. The patient had weight loss of 8 kg in the prior three months. Two years before admission, the patient was suspected to have BD because of recurrent anterior uveitis and treated with infliximab. The patient never developed oral or genital ulcers, arthralgia, or neurological complaints during follow-up. There was no family history of BD or consanguinity. A written informed consent was obtained from the parents of the patient.

show abstract

Cardiac Tumor in Juvenile Onset Behçet’s Disease: Case Report and Review of the Literature

Cited by 7 publications

References 9 publications

Juvenile Adamantiades-Behçet Disease

Juvenile Adamantiades-Behçet Disease

Pediatric Behçet's disease with cardiac valvular lesions: A case-based review

Is Immunosuppressive and Thrombolytic Therapy Really Effective in a Patient With Intracardiac Thrombosis and Pulmonary Artery Aneurysm due to Behçet’s Disease?

Contact Info

Product

Resources

About