Blaschkoid mastocytosis

Mastocytosis in children

“…Recently, a new variant of mastocytosis called blaschkoid pattern of mastocytosis has been described in the literature in a child where the lesions occur along the lines of blaschko. [30] Systemic Mastocytosis Systemic mastocytosis is more common in adults and is rarely seen in children. It is defined as mastocytosis occurring in at least 2 organs.…”

Cutaneous Mastocytosis in the Adult: What Lies Beneath

“…Mastocytosis is a rare heterogeneous group of hematopoietic disorders characterized by increased accumulation of mast cells in one or more organs. The most frequently involved are the skin but bone marrow, gastrointestinal tract, liver, spleen and lymph nodes may also be implicated 1 . The incidence is estimated in 1 in 1000 to 8000 patients.…”

Adult‐onset blaschkoid mastocytosis: A rare manifestation of an uncommon disease

“…Other rare variants include anetodermic, giant inguinal and suprapubic masses. 4,5 Blaschko's lines are a pattern of linear distribution of different nevoid and acquired diseases, which is hypothesised to be due to the phenomenon of mosaicism, that is two or more genetically distinct cell populations or clones are present in an individual derived from a single zygote. 6 When a group or a segment of these clonal cells are affected during embryonic or post-zygotic stage, they cause cells of skin to react and to manifest disease in the region concerned.…”