Bilateral Optic Nerve Hypoplasia with Normal Visual Acuity

Congenital disorders of the optic nerve: excavations and hypoplasia

“…When the ratio of DM to DD is greater than 3, ONH is suspected, and when it is greater than 4, ONH is very likely. which is commonly superior (causing a lower visual field defect), 79 can be identified by clinical observation, red free photography, 80 or by optical coherence tomography. 81 Reduced optic nerve diameter (from the normal range of 4-4.5 mm) measured by ultrasound has been described, and the diameter of the optic canal may be reduced.…”

Superior Segmental Optic Hypoplasia Found in Tajimi Eye Health Care Project Participants

“…This condition is ophthalmoscopically characterized by a relatively superior entrance of the central retinal artery, pallor of the superior optic disc, a superior peripapillary scleral halo, and thinning of the superior peripapillary nerve fiber layer. [1][2][3][4][5][6][7][8] Perimetry reveals an inferior altitudinal defect or an inferior sector defect connecting to the blind spot. Visual acuity is not affected in most cases.…”

Optic nerve axons: life and death before birth

“…Vision and associated features: Severe hypoplasia causes blindness, but in lesser degrees a variety of abnormalities have been described, with some patients having clinically normal visual acuity [131][132][133] although field defects in those cases with good acuity are common. 133 Visual acuity is determined largely by the size of the papillomacular bundle, not with the overall size of the disc; there is not a very close correlation between the size of the optic disc and the visual function.…”