Awake Blind Nasal Intubation in a Patient with Xeroderma Pigmentosum

Anesthetic management of a child with xeroderma pigmentosum

“…S ir —Xeroderma pigmentosum (XP) is a rare autosomal‐recessive inherited genetic defect in the UV‐radiation induced DNA repair mechanism, which is the characterized by sensitivity of the skin to all sources of UV radiation. Little information exists on the optimal anesthetic management (1,2).…”

“…Meyer (2) reported on difficult airway management in a patient with XP who presented with a squamous cell carcinoma of the tongue and enormous swelling of the tongue and massive scarring of the oral region.…”