Perioperative management of a patient with Xeroderma Pigmentosum: A case report

Webb, Leah M.; Chatterjee, Debnath; Brockel, Megan A.

doi:10.1016/j.epsc.2020.101710

Cited by 3 publications

(3 citation statements)

References 9 publications

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“…Such a tool is recommended for XP patients not to exceed 2-30 microW/cm 2 [ 8 ], corresponding to the weak radiation at dawn or sunset time. UV filters over lights and cameras could also be described [ 9 ], but caution should be taken given that the filters induce an uncontrolled change in the wavelength of the light and lead to instability at long exposure. Risks could also be limited by covering the rest of the patient´s body with drapes and towels during the intervention.…”

Section: Discussionmentioning

confidence: 99%

The therapeutic dental challenge of xeroderma pigmentosum patients: case report

Hanine¹,

Ghoul-Mazgar²,

Cherkaoui³

2023

Pan Afr Med J

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Xeroderma pigmentosum (XP) is a rare genetic disease characterized by a hypersensitivity to ultraviolet (UV) radiation leading to defective deoxyribonucleic acid (DNA) repair and predisposing to skin tumorigenesis. This paper reports the safe approaches used for the dental treatment of XP patients, controlling the ultraviolet (UV) sources at the dental office. An XP 29-year-old woman was referred for oral pain and sensitivity at the service of periodontology, UV rays were checked with a UV-meter. During the examination, the patient kept her sunglasses while the practitioner was dressed in dark colors using an anti-UV filter over the surgical light. Facial dark brown pigmentations, limited mouth opening, tumor resection scar on the tongue, moderate periodontitis, and dental caries were noticed. Moderate periodontitis and dental caries were diagnosed. Treatment was planned in collaboration with the dermatologist. Soft scaling and root planning were performed in short sessions and self-curing material was used for coronary fillings after caries removal. In taking care of XP patients, particular attention should be given by dental professionals to: i) the office management for a UV-safe environment; ii) the adoption of suitable dental care and safe biomaterials with short sessions and regular controls; and iii) the adoption of personal protections by patients and practitioners.

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Section: Discussionmentioning

confidence: 99%

The therapeutic dental challenge of xeroderma pigmentosum patients: case report

Hanine¹,

Ghoul-Mazgar²,

Cherkaoui³

2023

Pan Afr Med J

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“…Another consideration with these patients is the UV radiation sources in the operating room. The surgical spotlights, headlamps and laparoscopic light source emitted significant radiation; therefore, they must be covered with UV-filtering material (19). Since we could not provide such a material for our patient who was operated under emergency conditions, we had to operate him in an operating room with LED lights that do not emit UV radiation, and with an open surgical method.…”

Section: Discussionmentioning

confidence: 99%

Difficult Intubation and General Anesthesia Management in a Pediatric Patient with Xeroderma Pigmentosum Requiring Emergency Laparotomy

Önemli¹,

Şahin²

2022

JARSS

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“…Halothane, isoflurane and sevoflurane effect neucleotide excision repair and may worsen neurological symptoms. Fjauji reported postoperative neurological aggravation after sevoflurane anaesthesia in an adult patient already suffering from neurological dysfunction [5]. Hajijafari, Webb used sevofiurane without any untoward complication [6,7].…”

Section: Discussionmentioning

confidence: 99%

Klippel-Trenaunay Of The Child: Case Report

Lalwani,

Pandey,

Kashyap

2020

Genesis

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Xeroderma Pigmentosa (XP) is an autosomal recessive disorder, affected patients are extremely sensitive to ultra violet (UV) rays and have characteristic lesions in sun exposed areas viz head, face and neck. 25-30% of XP individuals develop neurological manifestations in infancy or second decade. In vitro studies and case reports suggests worsening of neurological status in XP patients after exposure to inhalational agents. We present successful anaesthetic management of a young boy presented to us for excision of squamous cell carcinoma of right eye lower lid. Perioperatively patient was covered and kept in dimlight. Anaesthesia was induced with fentanyl, propofol, atracurium and maintained with oxygen, air and sevoflurane. Shifted to dimlight ward with goggles to avoid photophobia and discharged after three days. In our case sevoflurane did not cause any adverse outcome. Further research is needed in this group of patients to know the effect of anaesthetic agents in worsening the disease course as these patients are frequently exposed to anaesthesia for various surgical lesions.

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Perioperative management of a patient with Xeroderma Pigmentosum: A case report

Cited by 3 publications

References 9 publications

The therapeutic dental challenge of xeroderma pigmentosum patients: case report

The therapeutic dental challenge of xeroderma pigmentosum patients: case report

Difficult Intubation and General Anesthesia Management in a Pediatric Patient with Xeroderma Pigmentosum Requiring Emergency Laparotomy

Klippel-Trenaunay Of The Child: Case Report

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