Atypical scleromyxedema with prominent nodular lesions associated with immune thrombocytopenia: An unusual presentation

López‐Lerma, Ingrid; Fernández‐Codina, Andreu; Hilari, H.; Ferrer, Berta; Selva-O’Callaghan, Albert; García‐Patos, Vicente

doi:10.1016/j.jaad.2014.07.004

Cited by 6 publications

(5 citation statements)

References 4 publications

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“…This atypical group was expected to include the least number of unclassified cases that do not conform to any of the two typical subtypes. However, this was not the case, and many patients were described by their authors as “atypical LM.” This might be attributed to the wide range of atypical presentations proposed by this classification (four subtypes within this small group, including a vague term called “not well‐specified cases”), denoting that the whole classification is not strict enough to easily include the newly reported cases.…”

Section: Diagnostic Criteria and Classificationmentioning

confidence: 93%

Lichen myxedematosus: diagnostic criteria, classification, and severity grading

Nofal

Amer²,

Alakad

et al. 2016

Int J Dermatology

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We propose two sets of diagnostic criteria to define the disease more precisely and to avoid confusion associated with the other classification. The first set comprises constant clinical and histopathological features that are always present in every case, and the second set includes associated features that were variably reported in some patients. LM is then subclassified according to the presence or absence of systemic manifestations into a systemic severe form (scleromyxedema) and a non-disabling, pure cutaneous form.

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Section: Diagnostic Criteria and Classificationmentioning

confidence: 93%

Lichen myxedematosus: diagnostic criteria, classification, and severity grading

Nofal

Amer²,

Alakad

et al. 2016

Int J Dermatology

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“…There were no symptoms associated in four reported cases (Table 1). [33][34][35][36][37][38][39][40][41]…”

Section: Figurementioning

confidence: 99%

Lichen myxedematosus: a rare group of cutaneous mucinosis

Cardenas-Gonzalez

Herz‐Ruelas

Candiani

2019

An. Bras. Dermatol.

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“…Nodular LM is characterized by firm, skin-colored nodules usually more than 6 mm in diameter with or without papules located on the trunk and extremities. Very few cases of nodular LM have been reported and the age of onset seems to be lower compared to APPM and DPLM [16][17][18].…”

Section: Nodular Lichen Myxedematosusmentioning

confidence: 93%

Papular mucinosis (papular lichen myxedematosus): Clinical and histopathological evaluation

Sharquie¹,

Jabbar²

2021

Our Dermatol Online

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Background: Papular mucinosis is a variety of mucinosis characterized by excessive production of mucin by fibroblasts and deposition in the dermis. It manifests itself with fleshy papules or plaques in different sites of the body and taking different clinical morphological cutaneous features. Objective: The objective is to report and evaluate the different clinical and histopathological features of the disease in Iraqi patients. Patients and Methods: This is a case series and a clinical descriptive study in which ten patients with papular mucinosis were reported during the period from 2012 through 2019. The age ranged from 4 to 56 years, with seven females and three males. Clinical evaluation regarding histories of the disease and examination was carried out. General investigation was done and skin biopsy for histopathological assessment was conducted. Results: Nine patients were adults, with their age ranging from 20 to 56 years, a mean of around 35 years, and only one 4-year-old child. It is a disease with a female predominance, as observed in 7 (70%) females. The common sites of involvement were the face but the rash may extend to affect the neck and upper arms. The rash appeared in the form of skin-colored or red fleshy papules and plaques or in diffuse erythematous orange peel-like forms. The rash was asymptomatic in most patients. The pathology of the disease clarified the diffuse deposition of mucin in the dermis, as was demonstrated with H&E staining. Conclusion: Papular mucinosis is a rare disease characterized by mucin deposition in the skin affecting mostly adult females. The face is commonly involved together with other areas such as the neck and upper arms, but the trunk and lower limbs are spared. It manifests itself with different clinical morphological cutaneous features. Papular granuloma annulare must be considered as an important differential diagnosis in all cases of papular mucinosis.

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Atypical scleromyxedema with prominent nodular lesions associated with immune thrombocytopenia: An unusual presentation

Cited by 6 publications

References 4 publications

Lichen myxedematosus: diagnostic criteria, classification, and severity grading

Lichen myxedematosus: diagnostic criteria, classification, and severity grading

Lichen myxedematosus: a rare group of cutaneous mucinosis

Papular mucinosis (papular lichen myxedematosus): Clinical and histopathological evaluation

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