Aplasia cutis congenita: approach to evaluation and management

Browning, John

doi:10.1111/dth.12106

Cited by 71 publications

(75 citation statements)

References 22 publications

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“…When performed, it shows an atrophic epidermis with loose fibrovascular stroma, edematous dermal stroma, or both [5]. A sonography of the lesion and a transfontanellar sonography should be done to rule out skull defects or cerebral abnormalities [7]. BACC can be visualized on prenatal sonography as a smooth cystic lesion without flow [8].…”

Section: Discussionmentioning

confidence: 99%

The Trichoscopic “Golf Club Set” Sign for Bullous Aplasia Cutis Congenita

Cutrone

Grimalt

2018

Skin Appendage Disord

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Section: Discussionmentioning

confidence: 99%

The Trichoscopic “Golf Club Set” Sign for Bullous Aplasia Cutis Congenita

Cutrone

Grimalt

2018

Skin Appendage Disord

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“…The decision to use medical, surgical or both modes of therapy depends primarily on size, dept, location of the defects and therapy of associated abnormalities. 5 This child had occlusive honey dressing, but in large defects ACC surgical repair including excision with primary closure, use of tissue expanders and rotation of flap to fill defects, skin and bone grafting may be required.…”

Section: Discussionmentioning

confidence: 99%

“…The treatments of ACC depend primarily on size, dept and location of the defect and therapy of associated disorders. 5 Variety of dressings both adhesive and non adhesive materials have been used. 6,7 Surgical repairs of large defects can be done.…”

Section: Introductionmentioning

confidence: 99%

Aplasia cutis congenita in a Nigerian child: A case report

Mava¹,

Yakubu²

2018

Nig. J. Paed.

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Aplasia cutis congenita (ACC) is a rare skin disorder, the cause is not known but intrauterine infections, drugs, chromosomal and genetic disorders, vascular compromise and trauma have been implicated. Clinically the diagnosis is made based on physical findings indicative of intrauterine disruption of skin development. We present an eighteen hours old neonate with Aplasia cutis congenita, this is aimed at creating awareness in view of the rarity of this condition. Conservative treatment of the ulcers has yielded excellent result but not without complication of acquired syndactyly, the child is being followed up for possible surgery to release the digits.

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“…La relación con malformaciones de cráneo y sistema nervioso central suele ocurrir en lesiones grandes (> 10 cm) 3 . Además, si es factible, se debe realizar el estudio de la placenta en busca de bandas amnióticas, malformaciones arteriovenosas e infartos.…”

Section: Comentariosunclassified

“…2). En grandes lesiones asociadas a defectos óseos, se recomienda la reconstrucción quirúrgica con cierre definitivo con colgajos locales, expansiones tisulares y craneoplastia [3][4][5] .…”

Section: Comentariosunclassified

Aplasia cutis congénita

Font¹,

Márquez

Lopez³

2015

Rev Pediatr Aten Primaria

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Aplasia cutis congenitaPresentamos el caso de un lactante de siete días diagnosticado de aplasia cutis congénita en su primera visita de control del recién nacido de Atención Primaria. La aplasia cutis congénita es una entidad poco frecuente (0,5-1/10 000 recién nacidos) que se halla en neonatos generalmente como hallazgo casual. Su localización más frecuente es el cuero cabelludo, a nivel del ápex. Pese a que su etiología es desconocida se ha relacionado con diferentes síndromes y malformaciones, que deben conocerse para realizar una buena exploración física, un uso racional de pruebas diagnósti-cas y un buen diagnóstico diferencial.We report the case of an infant with aplasia cutis congenita diagnosed on his first visit for control of the newborn in primary care. Aplasia cutis congenita is a rare entity (0.5-1/10,000 newborns) which is found in newborns usually as incidental finding. Its most common site is the scalp, at the level of the apex. Although its etiology is unknown it has been associated with various syndromes and malformations, which must be known for a good physical examination, a rational use of diagnostic tests and differential diagnosis. 357 CASO CLÍNICOLactante de una semana de vida que consulta para primera visita de control del recién nacido. Varón, fruto de una segunda gestación a término sin complicaciones y parto eutócico sin incidencias. La madre refiere una lesión de aproximadamente 1 cm de diámetro en el vértice del cuero cabelludo desde el momento del nacimiento.La exploración física evidencia la lesión de 1 cm de diámetro, de bordes limpios, sin signos de sobreinfección (Fig. 1). Ante la sospecha de aplasia cutis congénita (ACC) se realizó una radiografía de crá-neo y una ecografía cerebral transfontanelar, que fueron normales. El genograma no evidenció enfermedades genéticas, pero el padre también presentaba una zona de alopecia cicatricial en el vértice del cuero cabelludo, que refiere desde la infancia.

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Aplasia cutis congenita: approach to evaluation and management

Cited by 71 publications

References 22 publications

The Trichoscopic “Golf Club Set” Sign for Bullous Aplasia Cutis Congenita

The Trichoscopic “Golf Club Set” Sign for Bullous Aplasia Cutis Congenita

Aplasia cutis congenita in a Nigerian child: A case report

Aplasia cutis congénita

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