2006
DOI: 10.1590/s0004-282x2006000400024
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Abstract: RESUMO -Relatamos o caso de um homem de 40 anos de idade com doença de Fahr, definida por calcificações idiopáticas bilaterais em núcleos da base, que desenvolveu transtorno depressivo, tiques motore s e fônicos, comportamentos estereotipados tipo "punding" e alterações de personalidade com import a n t e s implicações sócio-familiares. Discutimos as manifestações psicopatológicas da doença de Fahr e a import â n c i a dos núcleos da base na determinação do comportamento humano. PALAVRAS-CHAVE: doença de Fahr,… Show more

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Cited by 10 publications
(16 citation statements)
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References 12 publications
(16 reference statements)
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“…2 FD is characterized by clinical heterogeneity and can be asymptomatic (more frequent among middle-aged patients) or associated with neuropsychiatric manifestations. [3][4][5][6][7] The physiopathological mechanism of FD is not completely understood. Anatomopathological alterations mainly were observed in small vessels, perivascular regions, neuroglia and neurons.…”
Section: Discussionmentioning
confidence: 99%
“…In the literature, varying manifestations of Fahr’s syndrome are described as memory disturbance, hallucination, delusions, personality change, and depression [2]; motor and phonic tics, stereotyped behaviors [3]; and extrapyramidal signs, such as Parkinsonism and paroxysmal nonkinesigenic dyskinesia [4]. Hoque et al [5] described a case of Fahr’s disease that presented with complex partial seizure and behavioral abnormalities.…”
Section: Discussionmentioning
confidence: 99%
“…Brain imaging shows the presence of whitish concentrated radiopaque regions according to the affected area and with well-defined areas, although the highest concentration is observed in a particular region of calcification, such as the basal ganglia (1)(2)(3) . Regarding the clinical findings on the disease, the literature data show that there are changes in social behavior and motor functions, as well as motor and phonic tics and inappropriate behavior according to the situation experienced (4) , features that imply modifications in speech and orofacial motor functions.…”
Section: Introductionmentioning
confidence: 99%
“…It is known that injury to brain areas, especially those involving the coordination of movements, maintenance of motor rhythm, and muscle tone, such as the basal ganglia region, highly affected by Fahr's disease, can result in changes in muscle function, changing stomatognathic functions. In this disease of oral expressiveness, the individual has difficulty or inability to express themselves through speech because of the difficulty in maintaining speech (4)(5)(6) . Thus, this study aims to report the case of a patient with Fahr's disease, seeking to describe the main stomatognathic characteristics and vocal aspects found.…”
Section: Introductionmentioning
confidence: 99%
“…Fahr's disease (FD), also called idiopathic striopallidodentate calcinosis, nonarteriosclerotic cerebral calcification or idiopathic basal ganglia calcification 1,2 , is a rare clinical entity characterized by movement disorders, dementia and behavioral disorders related to symmetric and bilateral calcifications of the basal ganglia. Sporadic and family cases have been reported [1][2][3] . FD should be differentiated from Fahr's syndrome.…”
mentioning
confidence: 99%