Adult Survivor With Repaired Complete Pentalogy of Cantrell

Mizelle, Katherine M.; Holtzlander, Melissa; Fatima, Ajaz; McConnell, Patrick I.; Splaingard, Mark

doi:10.1177/2150135114540181

Cited by 2 publications

(1 citation statement)

References 9 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…The survival rate was less than 0.8%. 16 However, it has also been reported that older children or adults had satisfactory surgical outcomes and no mortality, 17 18 19 potentially reflecting the condition of their cardiac malformations and differences in the severity of the disease in these patients. In some cases, the intracardiac malformation is not serious; the patient merely has a slight defect of the thorax and abdominal wall and a protruding heart.…”

Section: Discussionmentioning

confidence: 99%

Experience in the Treatment of Pentalogy of Cantrell with Artificial Materials in a Single Clinical Center

Wang

et al. 2021

Eur J Pediatr Surg

View full text Add to dashboard Cite

Objective To summarize experience in the treatment of pentalogy of Cantrell (POC) in our hospital and explore the effect of artificial materials in repairing sternal defects. Materials and Methods A retrospective analysis was performed on treatment of five children with POC treated by using the Gore-Tex patch and titanium mesh in the Department of Cardio-Thoracic Surgery, Children's Hospital of Chongqing Medical University, from January 2010 to January 2019. Results The concurrent conditions included double outlet of right ventricle (n = 2), ventricular septal defect (VSD) and atrial septal defect (ASD) (n = 1), VSD and ASD and patent ductus arteriosus (n = 1), and VSD and left ventricular diverticulum (n = 1) in five cases with POC. Color Doppler echocardiography and computed tomography (CT) + three-dimensional (3D) reconstruction of the thorax and abdomen were performed preoperatively. The cardiac malformation was corrected according to color Doppler echocardiography, and a Gore-Tex patch was used to repair the pericardial defect. Titanium mesh was made according to CT 3D reconstruction with a 3D printing mold to repair sternal defects. All patients underwent a one-stage operation, all hearts were eventually repositioned, no deaths occurred after the operation, and follow-up was performed for 6 months to 2 years. The patients recovered well, and the exterior thorax was normal. Conclusion The diagnosis of POC is not difficult. The priority of surgical treatment for POC is to obtain satisfactory corrections of cardiac malformation. The repair of the pericardial defect with the Gore-Tex patch and the sternal defect with the titanium mesh can make the heart return to the mediastinum, reduce the pressure on the heart, reduce the surgical trauma, reduce the difficulty of repairing the sternal defect, and optimally restore the exterior thorax.

show abstract