Acquired progressive lymphangioma as a flat erythematous patch on the abdominal wall of a child

A case of extensive acquired progressive lymphangioma

“…Our patient was also much younger than any of the other reported cases, in adults or children, with 24 of the 31 confirmed APL cases in the literature in adults (aged 27‐90) and 7 in older children (aged 5‐17) . Adults have also tended to have larger lesions, (0.3‐60 cm in greatest diameter), whereas children have generally had smaller lesions (2‐16 cm), which suggests that this may be different clinical entities in adults and children, despite histologic similarities.…”

“…This case of APL is different from prior reports. Reported patients with APL have ranged in age from 5 to 90 years old, with a median age of 54 . Prior cases generally report gradual growth, but our patient was young and experienced quick progression in a slightly atypical distribution, with a large segment of the body being involved.…”

“…Extensive progression has been reported in only one prior case, although that was in an adult. Because APL in most cases is less extensive and progressive, surgical excision or systemic treatments such as antibiotics and corticosteroids have been reported to be effective. Because of the extensive nature and ongoing rapid progression at such a young age, exploration of other treatment options was necessary in our patient.…”

“…The pathogenesis of this uncommon vascular anomaly of lymphatic type is not completely understood, and several theories have been proposed. Some authors have suggested hormones as a potential stimulus, given one case of expansion in a peripubescent patient . Considering frequency of preceding trauma, inflammatory—rather than neoplastic—etiologies have also been proposed .…”

Linfangioendotelioma benigno: diagnóstico y tratamiento

“…Se trata de un proceso de cará cter reactivo y que parece estar condicionado por estímulos hormonales 6 , hecho que explicaría su frecuente aparició n en la adolescencia y la pubertad.…”