Accessory and ectopic scrotum with VATER association

Surgical management of perineal masses in patients with anorectal malformations

“…Masses of the perineum in infancy and childhood primarily consist of accessory or ectopic scrota or perineal lipomas [1][2][3][4][5]. Surgical excision of these lesions is generally straightforward.…”

Topical testosterone in scrotal agenesis

“…This may suggest an abnormal migration of the labioscrotal folds, which in a normal case would result in ectopic scrotum. The presence of testis in the same location is further suggestive of the abnormal migration, as the inferior gubernaculum is normally inserted in to the labioscrotal folds to facilitate the descend of the testis [9].…”

Inguinal Ectopic Scrotum, Anorectal Malformation with Sacral Agenesis and Limb Defects: An Unusual Presentation

“…Simultaneously, at around the 5th week, gubernaculums develops as a condensation of me- senchymatous tissue extending from the mesonephros to the abdominal wall. The inferior gubernaculum inserts into the labio-scrotal swellings to descend the testis [3].…”

“…However, fetal akinesia due to fetal abnormalities or maternal disorders can lead to arthrogryposis (which may have joint contractures and club foot) and may lead to development of contractures which can lead to abnormal developments by counter compression mechanisms. Thus the primary event leading to this set of abnormalities is still uncertain [3][4][5].…”