A rare case of accessory maxilla: a case report and literature review of Tessier no. 7 clefts

Abstract

Bilateral Tessier no. 7 clefts are rarely reported in the literature. Here, we describe the presence of accessory maxilla with supernumerary teeth in a patient who exhibited bilateral Tessier no. 7 clefts; the diagnosis was established based on the patient’s history, clinical presentation, and computed tomography images. A review of the available literature revealed 24 patients with Tessier no. 7 clefts from 2000 to 2020, including our patient. The most common clinical manifestation in patients with Tessier no. 7 clefts comprises bilateral facial clefts. Additionally, Tessier no. 7 clefts are more frequently found in boys or men, rather than in girls or women. The presence of an accessory maxilla with supernumerary teeth in a patient with bilateral Tessier no. 7 clefts is extremely rare. Early detection of craniofacial abnormalities is important, because it may influence patient prognosis and management.

Bilateral Tessier no. 7 cleft with an accessory maxilla and osseous choristoma: a case report

“…7 cleft was bilateral facial clefts. Only three patients exhibited unilateral accessory maxilla [ 14 ]. In the literature reviewed, there was not any report of osseous choristoma associated to these kinds of anomalies.…”

Accessory Maxilla in a Tessier 07 Cleft - A Case Report

“…[ 3 ] Isolated macrostomia with maxillary duplication is rare and the entity is more commonly associated with other forms of facial clefts. [ 1 , 2 ] Owing to this multitude of defects, patient was assessed and operated early in life to ensure the normal development of speech, eating, facial appearance and possible social interaction. Although some advocate delaying such correction and creation of new commissure when there is a need of mandibular and zygomatic repair, ensuring coordinated growth and proper feeding becomes paramount.…”

“…7 cleft. [ 1 , 2 ] Oblique facial clefts are a rare craniofacial deformity that can manifest in a variety of patterns and severity. Macrostomia is a unique type of oblique facial cleft that results in a large mouth by involving commissures of the involved side.…”

Síndrome oculoauriculofrontonasal: caracterização fenotípica

“…Em adição, a TC revelou a presença de uma estrutura óssea anômala contendo dentes molares, localizada abaixo do corpo do zigoma e anexada ao processo zigomático do osso temporal, compatível com uma maxila acessória. Maxilas acessórias são clinicamente variáveis e podem ocorrer na forma isolada ou associada a outras anomalias (HOU et al, 2015;SUN et al, 2020). Na maioria dos casos ela é unilateral, afetando principalmente indivíduos do sexo feminino, e está frequentemente relacionada com a ocorrência da fissura Tessier 7 (BORZABADI-FARAHANI et al, 2013;HOU et al, 2015;SUN et al, 2020).…”

“…Maxilas acessórias são clinicamente variáveis e podem ocorrer na forma isolada ou associada a outras anomalias (HOU et al, 2015;SUN et al, 2020). Na maioria dos casos ela é unilateral, afetando principalmente indivíduos do sexo feminino, e está frequentemente relacionada com a ocorrência da fissura Tessier 7 (BORZABADI-FARAHANI et al, 2013;HOU et al, 2015;SUN et al, 2020). Além das fissuras raras e da maxila acessória, foi possível observar a presença do osso nasal ectópico.…”