A congenital cystic pulmonary airway malformation occurring together with both an extralobar pulmonary sequestration and an esophageal duplication cyst

Dewberry, Lindel C.; Trecartin, Andrew; Galambos, Csaba; Hilton, Sarah A.; Dannull, Kimberly; Zaretsky, Michael V.; Behrendt, Nicholas; Galan, Henry L.; Marwan, Ahmed I.; Liechty, Kenneth W.

doi:10.1002/ccr3.2455

Cited by 2 publications

(1 citation statement)

References 27 publications

(53 reference statements)

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“…ELS is almost discovered on regular antenatal ultrasonographic screening or incidentally detected in later life. A few of ELS are identified accompanied with other congenital anomalies, such as congenital diaphragmatic hernia (CDH) or diaphragmatic eventration, cardiac defects, foregut anomalies, and congenital pulmonary airway malformation (CPAM) 11–14 . The previous study demonstrated that ELS patients might remain asymptomatic throughout life without any surgical intervention 1 .…”

Section: Introductionmentioning

confidence: 99%

The clinical management of extralobar pulmonary sequestration in children

Huang

Habuding

Miao

et al. 2021

Pediatric Pulmonology

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Introduction The treatment of extralobar pulmonary sequestration (ELS) remains divergent. This study aims to demonstrate the characters of ELS in children for optimal clinical management in the future. Material and Methods A retrospective analysis was conducted for ELS patients' treatment in our center from January 2013 to April 2020. Results In total, 85 patients were included, containing 70 upper‐diaphragmatic, 7 intra‐diaphragmatic, and 8 infra‐diaphragmatic ELS. Eight patients' pathology results showing inflammation without symptoms preoperation and two patients had chest pain for torsion. All the upper‐diaphragmatic and intra‐diaphragmatic ELS patients accepted thoracoscopic surgery resection. The intraoperative operation time and blood loss volume of intra‐diaphragmatic ELS were significantly more than that of the upper‐diaphragmatic (40.14 ± 9.92 vs. 23.07 ± 6.79 min; 9.29 ± 3.45 vs. 3.18 ± 4.94 ml; all p < .05). No chest tubes were inserted in both subgroups. No complications were found in the postoperative follow‐up of operative ELS patients at least 3 months. A total of eight infra‐diaphragmatic ELS patients except for one (7/8) had conservative therapy and follow‐up by the outpatient clinic or phone call eventually. There were no symptoms occurring and no size increasing of observation infra‐diaphragmatic ELS. Conclusions The ELS has the potential risk of infection and torsion in this study. Thoracoscopic surgery might be optimal management of upper‐diaphragmatic ELS for its minimal invasion and low perioperative risks, which could be developed into a day operation with safe and quick recovery. The intra‐diaphragmatic and infra‐diaphragmatic ELS need a larger sample size and multiple center data to get a better management approach.

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Section: Introductionmentioning

confidence: 99%

The clinical management of extralobar pulmonary sequestration in children

Huang

Habuding

Miao

et al. 2021

Pediatric Pulmonology

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Neonate with congenital pulmonary airway malformation concurrent with enteric duplication cyst: a case report of a rare anomaly

Krishnan,

Schmoke,

Nemeh

et al. 2023

Journal of Surgical Case Reports

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A congenital pulmonary airway malformation (CPAM) occurring concurrently with an enteric duplication cyst is a rare anomaly. Definitive management for both abnormalities is usually surgical resection. We present the uncommon case of a neonate with a CPAM and ileal duplication cyst, including pre-natal and post-natal workup. The patient was brought to the operating room for laparoscopic duplication cyst excision at 3 months of age. The patient returned to the operating room for a thoracoscopic right lower lobectomy at five months of age. This case presents a rare congenital anomaly with the concurrent presentation of a CPAM and enteric duplication cyst, with both being successfully excised minimally invasively.

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A congenital cystic pulmonary airway malformation occurring together with both an extralobar pulmonary sequestration and an esophageal duplication cyst

Cited by 2 publications

References 27 publications

The clinical management of extralobar pulmonary sequestration in children

The clinical management of extralobar pulmonary sequestration in children

Neonate with congenital pulmonary airway malformation concurrent with enteric duplication cyst: a case report of a rare anomaly

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