A Case of Woolly Hair Naevus

Wooly hair nevus

“… 1 , 2 Subsequently, Post divided woolly hair in 3 types (Type 1-no association with scalp disorders or loss of body hair; Type 2-associated with linear verrucous epidermal nevus; Type 3-acquired, in young adult patients; the hair is curly, dark and short, similar to pubic hair). 1 , 3 , 4 , 6 Woolly hair nevus is a rare, non-hereditary form of woolly hair. It is easily distinguished from the generalized form, for it affects only a few well defined areas of the scalp.…”

“… 1 - 3 In Post’s classification, wooly hair nevus can be subdivided in three types: Type 1-no cutaneous involvement; Type 2-associated to linear verrucous epidermal nevus; Type 3-acquired, in young adult patients, where scalp hair has the same features of pubic hair. 1 , 3 , 4 It is estimated that 50% of the cases of woolly hair nevus are associated to linear verrucous epidermal nevus on the ipsilateral upper limb, face or neck. 1 , 5 The authors describe a case of woolly hair nevus Post’s type 2, developed during childhood.…”

Woolly hair nevus type 2: Rare entity

“…Woolly hair was first discovered in a European family by Gossage in 1907. [2] It can be either sporadic or genetic. Hutchinson et al .…”

Woolly Hair Naevus with Ocular Involvement

“…A family with the dominant inheritant type of WHD and cataracts [6] and a case of woolly hair naevus with a persistent pupillary membrane [2] have been described. In the present case, anomalies of both mesodermal and ectodermal tissue were found in the eye.…”