Urticaria is a common dermatologic disorder characterized by pruritic wheals, often surrounded by reflex erythema that resolves within 24 h. These skin manifestations may be accompanied by angioedema, or sudden swelling of the underlying dermis, which usually resolves within 72 h. Urticaria can be caused by various agents such as allergy, infection, or physical stress that provoke mast cell degranulation. However, yellow urticaria is an exceptional event that occurs in patients with hyperbilirubinemia due to liver or biliary diseases and most commonly in cirrhosis.