Case 2/2017 - Cor Triatriatum, without Clinical Manifestation, in A 6-Year-Old Girl

Cor triatriatum sinister with left anomalous pulmonary venous return to innominate vein

“…Cor triatriatum sinister is classified, according to Lam (1962), as type A, without associations, as in the present case; A1, in which the atrial septal defect occurs in the proximal chamber (50%); A2, in which the atrial septal defect occurs in the distal chamber (10%); B, in which the pulmonary veins drain into the coronary sinus (1%); and C, when there is total anomalous pulmonary venous drainage (5%). 4,6 Since the first surgical approach in 1956 by Lewis et al, surgery is the treatment of choice in symptomatic patients with cor triatriatum sinister. This case highlights the association between cor triatriatum sinister, left upper and lower anomalous pulmonary venous return to the innominate vein through the vertical vein and patent foramen ovale.…”

(Catheter based therapy of cor triatriatum sinister - case report)

“…Štandardným postupom je kardiochirurgická liečba, v posledných rokoch sa však úspešne uplatňuje aj transkatétrová liečba tejto zriedkavej vrodenej srdcovej chyby u detí aj dospelých. 4,5,9,10 Záver Katétrová liečba CTS s balónovou dilatáciou je vhodnou alternatívou kardiochirurgickej operácie, ak sú priaznivé anatomické podmienky. Popisovaný prípad CTS typ A s pokročilým klinickým nálezom, prejavujúcim sa kardiálnou dekompenzáciou a ťažkou pľúcnou hypertenziou, sme úspešne vyriešili perkutánnou katétrovou intervenciou.…”