Aneurisma de artéria poplítea como manifestação da doença de Behçet descompensada

Abstract

Behçet's disease consists of a systemic vasculitis that affects veins, arteries and capillaries, but predominantly small vessels. Veins and medium-and large-caliber arteries are rarely involved; however, arteries are less involved than veins. In this paper the authors present a case of popliteal artery aneurysm in a patient with decompensated Behçet's disease. We discuss clinical, radiological and surgical aspects of patients with this inflammatory systemic disease who present important peculiarities.Key words: Behçet's syndrome, aneurysm, popliteal artery. ResumoA doença de Behçet consiste em uma vasculite sistêmica que acomete veias, artérias e capilares, mas predominantemente pequenos vasos. Raramente há o envolvimento de veias e artérias de médio e grande calibre, sendo as artérias menos acometidas que as veias. No presente trabalho, os autores apresentam um relato de caso de aneurisma da artéria poplítea em um paciente com a doença de Behçet descompensada. Discutem-se os aspectos clínicos e radiológicos e o manejo cirúrgico dos pacientes com essa doença inflamatória sistêmi-ca que apresentam peculiaridades importantes.Palavras-chave: Síndrome de Behçet, aneurisma, artéria poplítea.

Tratamento endovascular de aneurismas da aorta em pacientes com doença de Behçet: relato de dois casos

“…If really necessary, surgeries should be performed when the disease is totally controlled with corticoids and immunosuppressants, because any intervention may lead to posterior complications, such as new occlusions, aneurysms or pseudoaneurysms. 16 In emergency cases, as a rupture, the remission state of the patient should be reevaluated. It has been shown that, before intervention, the attack dose of corticoids/immunosupressants in bolus (e.g., prednisolone) may decrease perioperative and postoperative vascular complications.…”

Endovascular treatment in Behçet’s disease: an integrative review

“…2 Behçet's disease is rare, chronic, relapsing, inflammatory, and multisystemic 3,4 and can provoke mucocutaneous, ocular, vascular, cardiac, neural, and gastrointestinal manifestations. 5 The international diagnostic criteria for BD are recurrent oral ulceration (apthous ulcerations that recur three or more times in a 12-month period) and at least two of the following: recurrent genital ulceration (apthous ulcer or scabs), ocular lesions (anterior uveitis or retinal vasculitis), cutaneous lesions (erythema nodosum, pseudofolliculitis, or papulopustular lesions), and pathergy (skin hyperreactivity test in response to a minimal trauma, with readings in 24-48 hours) 6,7 Vascular involvement is one of the primary predictors of morbidity and mortality in BD, with a negative impact on prognosis. 8 Behçet's disease is considered a systemic vasculitis when vascular involvement is present.…”

Tratamento endovascular na doença de Behçet: uma revisão integrativa

“…The international diagnostic criteria for BD are recurrent oral ulceration (apthous ulcerations that recur three or more times in a 12-month period) and at least two of the following: recurrent genital ulceration (apthous ulcer or scabs), ocular lesions (anterior uveitis or retinal vasculitis), cutaneous lesions (erythema nodosum, pseudofolliculitis, or papulopustular lesions), and pathergy (skin hyperreactivity test in response to a minimal trauma, with readings in 24-48 hours) 6 , 7 Vascular involvement is one of the primary predictors of morbidity and mortality in BD, with a negative impact on prognosis. 8…”

“…Os critérios diagnósticos internacionais da doença são ulceração oral recorrente (ulcerações aftosas que recorrem três vezes ou mais em um período de 12 meses) e mais dois dos seguintes: ulceração genital recorrente (úlcera aftosa ou escaras), lesões oculares (uveíte anterior ou vasculite retiniana), lesões cutâneas (eritema nodoso, pseudofoliculite, lesões papulopustulosas) e patergia (teste de hiper-reatividade cutânea em resposta a um trauma mínimo, com leituras em 24-48 horas) 6 , 7 . O envolvimento vascular é um dos principais preditores de morbidade e mortalidade da doença, afetando negativamente o prognóstico 8 .…”