Caso 2/2010 - lactente de 5 meses, do sexo masculino, com comunicação interventricular subpulmonar e coarctação da aorta

Abstract

Congenital cardiopathies; ventricular septal defect, aortic coarctation, pulmonary artery /abnormalities. trunk and the pulmonary arteries demonstrates the presence of pulmonary flow directly from the left ventricle to the right ventricular outflow tract, as in the subpulmonary location of the ventricular septal defect. Differential diagnosisAll other acyanotic congenital cardiopathies with left-toright shunt must be recalled, such as interatrial communication and patent ductus arteriosus, as long as they present a marked hemodynamic effect, which occurs, however, at more advanced ages. This alteration of marked dilatation of the pulmonary trunk is also seen in cyanotic cardiopathies with pulmonary hyperflow, such as total anomalous pulmonary venous connection. Diagnostic confirmationThe clinical elements were decisive for the diagnosis of the ventricular septal defect and aortic coarctation. The echocardiogram confirmed the presence of a ventricular defect with a direct connection with the pulmonary valve in a subpulmonary location, measuring 10 mm in diameter, in addition to the aortic coarctation in the isthmus region, measuring 3 mm in diameter, in relation to 7 mm of the ascending aorta and 5 mm of the aortic arch. The right ventricle was not dilated, considering the preferential flow from the left ventricle to the pulmonary artery tree. The left ventricle was enlarged and the left ventricular function was preserved (LVEF: 68%, Ao: 14, LA: 18, LV: 27) (Fig.2). ManagementAt surgery, the resection of the aortic coarctation in terminoterminal anastomosis with the aortic arch resulted in an adequate diameter of the region. The 10-mm subpulmonary or committed ventricular septal defect was closed through an incision in the pulmonary trunk, using a bovine pericardial patch. The heart failure condition was resolved. CommentsThe marked dilatation of the pulmonary trunk is seldom detected in infants, even in those with cardiopathies with marked pulmonary hyperflow. This anatomical confirmation, in this case, was due to the direct flow from the left ventricle to the pulmonary artery tree, through the ventricular septal defect. Moreover, this defect, when doubly committed to the great vessels, pathogenically explains the concomitant existence of aortic coarctation, considering the increased Clinical dataThe patient remained asymptomatic up to three months before, when he started to present fatigue even at rest, which grew progressively worse.Physical examination: the patient was tachydyspneic, had normal skin color, ample pulses in both upper extremities and decreased in the lower extremities. Weight was 5,130g. The blood pressures in the right upper limb and right lower limb were 150/80 and 100/80 mmHg, respectively. HR: 130 bpm. The aorta was not palpated at the suprasternal notch. The patient presented slight precordial impulses at the left sternal border and the ictus cordis was diffuse and palpated at the 5th intercostal space on the hemiclavicular line. Heart sounds were hyperphonetic and there was a holosystolic...