Involução tardia de rabdomioma obstrutivo da valva mitral

Abstract

Potential Conflict of InterestNo potential conflict of interest relevant to this article was reported. Sources of FundingThere were no external funding sources for this study. Study AssociationThis study is not associated with any post-graduation program.A male patient had presented signs of mitral valve obstruction since birth (fatigue during nursing, left atrial enlargement, diastolic gradient = 7 mmHg), which then regressed since 9 months of age. Masses identified at the mitral valve echocardiogram, right ventricular septum and left anterior papillary muscle led to a diagnosis of rhabdomyoma. Currently 14 years of age, the patient performs normal physical and mental activities. A late involution of the mitral valve mass was observed, partial at 5 years and total at 14 years of age. The mass measured 15x14mm up to 28 months of age, 14x11mm at 5 years and 12x10mm at 8 years of age. The other masses, which were non-obstructive, decreased. The expectant management showed a peculiar late involution of the rhabdomyoma.