“…In its development, it leads to the loss of hearing acuity in a few months, and this loss may be permanent in case the diagnosis is delayed, thus depriving the patient from the treatment. The atypical form usually involves the entire ocular structure, leading to recurrent episodes of conjunctivitis, episcleritis, uveitis, optic disc edema and retinal vasculitis (2)(3)(4)(5). Evidence of systemic vasculitis are found in 50% of patients, leading to a worse prognosis from the systemic point of view (3,6) .…”