Primary ciliary dyskinesia is a rare genetic disease. It is an autosomal recessive inherited disease. This rare disease affecting the respiratory system exposes the child to numerous new and, simultaneously, difficult situations that would be a significant challenge in the normal functioning for an adult.Nursing care over the patient suffering from primary ciliary dyskinesia creates numerous nursing problems for the patient treated both in home conditions as well as hospital ones. Good knowledge of the patient, his or her ailments, attitude towards the disease as well as planned and implemented treatment methods play an important role. It is essential to collect as much information about the child and his or her family as possible to plan care over the patient properly. The theory of Marjory Gordon may be helpful in this issue.